Quick Foreword: The Palace, (and before that, The Terrace) remains the best board to get into serious discussions regarding Peregrine. The Terrace is run by long time Peregrine champion, TerryGD. Due to the “Members Only” format, this board is top notch without any of the BS that can permeate other forums. This compilation is not 100% complete, I have left some of Golfdad’s less science-oriented messages at the Palace.

Thank you for visiting.

 

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Generally,

BLUE TEXT = DR. PHILIP THORPE

GREEN TEXT = DR. ALAN EPSTEIN: COTARA (TNT) and VEA

BLACK TEXT = ONCOLYM

ORANGE TEXT = GENERAL TOPICS AND/OR OTHER ITEMS

 

THE GOLFDAD MONOLOGUES

 

11/17/1998

Rutuxan:

Idec-C2B8 (Rituxan): This is a chimeric antibody directed against a B-cell specific antigen expressed on NHL cells. The target binding site of this antibody appears to allow several favorable biological effects, including mediation of complement-dependent lysis of malignant cells (a natural killing method mediated by serum proteins found in the course of many infectious states), the ability to provoke antibody-dependent cell killing (another natural consequence of binding antibodies to foreign cells) and the Rituxan antibody can directly inhibit the proliferation of NHL cells. Hence, these properties may be sufficient to not seek any radiolabel (which adds direct killing power to the vicinity of cells that bind the radiolabeled antibody), and allows its use as a "naked" antibody, although high concentrations (perhaps on the order of gram amounts) need to be infused.

 

Initial Phase I trials (and subsequent studies) were conducted in patients who eventually failed further chemotherapy and had few alternative therapies. The use of this antibody is attractive because of its structure (chimerized, therefore little impact on patients developing antibodies to Rituxan), the fact that it is not coupled to any toxic material (such as a radioactive isotope or drug) and can be administered repeatedly with few toxic side effects, other than eventual depletion of normal B-cells (which are needed for proper immune protection of the patient). The effects on immune cell depletion and function can be closely monitored. To summarize the early results in brief fashion (how can golfdad ever do that?)...a total response rate of about 45-50% was observed in patients with refractory, low-grade lymphoma. It must be emphasized that complete and partial responses are not entirely the same quantities between different clinical groups, but in general, in the lymphoma studies, a complete response requires no evidence for any disease for at least 1 month, whereas a partial response in normally considered to be a reduction of anywhere between 50-70% of tumor volumes measured by various parameters (dimensions off of radiograph films, CT scans, etc). However, many descriptions by academic physicians hedge different terms using phraseology like a "marked reduction", "although not significant, about 25% less disease", and remarks like that...but us simple folk know what we want to see: (1) percent of complete response, (2) percent of partial responses, (3) duration of the remission (time to treatment failure or time to relapse), and (4) overall survival. These early studies, like most Phase I set the dose, schedule and probable patient effects to monitor and watch for as the trials progress. They settled on about 750 mg/patient (depending on body size) once a week for 4 weeks, observed a fairly rapid depletion of B-cells and malignant cells (normal B-cell numbers would return in about 3-6 months) and the clinical responses lasted about 8-12 months, depending on the study reported. Low doses of the antibody resulted in some clinical responses that were encouraging but not impressive. Only a few patients with intermediate or high-grade lymphoma were attempted in the early trials. Responses tend to favor patients with follicular disease (a kind of localized network of webbed malignant cells, strung together in lymph node structures). The half life of the antibody is rather long...and increases to nearly 20-30 days as the number of infusions of the antibody increase. They also conducted a small Japanese study in Phase I at the Japan NCI and observed about a 40% response rate in relapsed patients.

 

The company quickly moved to Phase II trials in a multi-center study (31 centers, about 170 patients) and used the 750 mg/dose (approx) and 4 weekly doses as the gold standard. They observed a 48% total response rate (note that this was 6% complete response and 42% partial response, where a complete response was defined as complete clearing of the bone marrow and nodal sites and partial was a reduction of 50% or more) with a duration of response of about 13 months. Toxicity was mild and the effects on B-cell depletion were expected and monitored.

The company also performed studies in Europe and Australia and tested the product in more aggressive forms of lymphoma, including intermediate and high-grade lymphomas (diffuse large B-cell lymphoma, mantle cell lymphoma). They performed a prospective randomized Phase II study including patients if they were in first or second relapse, refractory to initial therapy, or elderly (>60 yo) and not previously treated. The patients received 8 weekly infusions of Rituxan at 750 mg/dose in one arm of the study and the patients in the other arm got one dose of 750 mg/dose followed by 7 weekly infusions of 1000 mg/dose (approx). 54 patients were evaluated, with 5 complete responses (10%) and a partial response of 22%, with an average duration of response of about 8 months, suggesting that this modest clinical activity (in my opinion) needed to be combined with chemotherapy...or this form of therapy limited mainly to low-grade lymphoma. I did not find any parameters that may "predict" for patients with high-grade lymphoma who would respond to this form of therapy (that is, how do you determine those 17 patients out of the 54 before starting therapy; is there any biological parameter you could measure, like extent of antibody binding to lymphoma cells, or??).

 

The company has recently reported pilot studies where Rituxan was combined with CHOP chemotherapy in patients with previously untreated intermediate and high-grade lymphoma (I will refrain from marketing remarks like..."in an attempt to break into that cohort of patient numbers"...). Rituxan was given on day 1 (750 mg/dose) followed a couple of days later by the usual CHOP chemo cycle and these cycles were repeated 6 times. Of the 30 evaluable patients, they reported a 63% complete response rate and 33% partial response. The authors do not clearly state whether this is better than what they would have observed using CHOP alone (with no Rituxan) on patients receiving their first chemotherapy, but I believe CHOP therapy alone in this grade of lymphoma would have resulted in about a 65% response rate...suggesting that this combination therapy may be of benefit as front-line therapy. But since they don't say it...I won't say it. Clearly these studies are continuing.

A multicenter study has also been performed with Rituxan combined with alpha-interferon (a protein produced by lymphocytes that modulate a variety of immune functions, including upregulation of cell antigens, direct antiproliferative effects on tumor cells, inhibition of cellular products that assist tumor growth and on and on). This study included 26 low-grade lymphoma patients that were refractory to therapy and treatment consisted of modest amounts of interferon given several times a week followed by 4 weeks of the gold standard Rituxan therapy. 8% complete response and 50% partial response was noted...and I suspect these studies will fade away...

 


Bexxar:

Anti-B1 antibody (Coulter). This is a different antibody targeted to the CD20 antigen of B-lymphocytes and is used as a radiolabel conjugate and is the direct correlate of radioimmunotherapy currently in use by TCLN and its Lym-1 antibody (to be described later). This form of therapy is championed by M. Kaminski and the group at Ann Arbor, Michigan and in my opinion, these people strongly believe in the clinical efficacy and approaches they use in treatment with this reagent. As you will see...they are willing to push the envelope in attempting to make this a front-line therapy for NHL.

 

Initial studies of Phase I focused upon the use of the I-131 (will confine remarks to iodine-based radiotherapy) conjugated to the B1 antibody and like all Phase I studies, they were limited to patients in dire need of further therapy with few alternatives. Studies defined the parameters of safety, dose and with this form of leukemia, one could look for therapeutic results. There are caveats to this form of therapy (radiolabel) not found with the use of naked antibodies...since we are delivering radiation to target sites in the body, and the toxicity will be limited by effects on normal tissue no different than observed for whole body irradiation, targeted beam radiotherapy or chemotherapy with toxic agents. Initial studies have to determine that the radiation uptake by areas of tumor is greater than that of normal organs and close monitoring of vital blood counts, effects on bone marrow, GI tract, central nervous system, etc is necessary. The logistics and expenses of this form of therapy can be extensive.


Pilot studies in 34 patients with NHL were performed several years ago and the dosimetry was established (conditions under which one could accurately estimate the amount of radiation being delivered to critical areas containing lymphoma). Hematologic toxicity was limiting and doses were escalated until about 750 rads (a measure of radiation being actually deposited in tissue) was found to be the upper limit, and represented about 50-75 mCi of radioactive material. A single dose of B1 (when I say B1, it is always radiolabeled with I131) was given as therapy, and of the 28 patients that could be evaluated, about 50% achieved a complete response (see earlier definitions) and a partial response (Bexxar studies usually use 50% reduction as partial) in 8 patients. The median duration of remission was about 16.5 months. These results could be broken down further in that of the 28 patients, 21 patients were low-grade or transformed NHL and of these patients, 19/21 responded and of the 7 intermediate-grade lymphoma patients, 3 responded. Hence, again, as with most therapies, better responses were observed in the low-grade lymphomas.

 

A comment on these initial studies is warranted. Radiotherapy with antibodies tends to unlease his hematologic effects due to resident time in the bone marrow...and if bulky disease or extensive bone marrow involvement is present, then non-specific toxicity will increase, just because of the targeting of the antibody. This is a common event in higher stage disease (say III and IV) because the bulk of the disease is not confined to discrete areas, such as lymph nodes. Hence, not only are there different risk factors than observed for the use of naked antibody, the whole system becomes complex in considering specific sites of disease and effects of the radiolabel...something to keep in mind.

These initial studies were reported a couple of years later (in a recent paper in Journal of Nuclear Medicine) and described results of 34 patients. The maximum tolerated dose was established as about 750 rads and in line with intuition, the patients who received higher doses of the therapy and responses were as described above. Some patients developed antimouse antibodies (since this antibody is mouse), with additional data that complete responses averaged about 13 months and the median duration of response for all patients who did respond about 11.5 months.

This group quickly took this form of therapy to the front line in several respects. First, the final Phase I/II results were reported this spring and involved 59 patients (28 low grade, 14 transformed low-grade, and 16 intermediate and high grade lymphomas). The median number of prior chemotherapies was 4 and remember that these studies involve patients who are non-responsive to further chemotherapy. Without intervening for bone marrow loss (for example, will discuss autologous bone marrow transplantation below), the therapeutic dose remained at about 750 rads. 24/28 of the low-grade patients responded and a complete response was observed in 46% of these patients. The mean tumor dose was about 14.5 times the whole body dose, meaning that localization to the tumor was good and much higher than that received by normal tissues, on the average. 15% of the patients developed antimouse responses which can limit further therapy. To be honest, I could not calculate how the intermediate grade patients fared on this therapy, since the given numbers (ASCO) were confusing to my trained eye.

 

However, the power of clinical funding for this therapy is apparent. Also reported this spring are several other aggressive moves with B1 antibody. For example, the Michigan group showed that NHL patients who relapse from the initial B1 therapy (from the Phase I/II described above) can be retreated. 13 patients were retreated and of these 13, 12 responded to the initial therapy....described above. 11 of these patients were from the low-grade NHL group (suggesting that the intermediate grade patients above did not do well?) and of these 13, 8 responded to re-treatment with a median duration of about 8 months. 4 of the 13 had a complete remission (second remission) of about 10 months. Again, it was noted that the higher the dose received (for whatever reason), the likelihood of response was greater...hence, this strategy was modestly successful, in that re-treatment of relapse patients can be attempted with some degree of confidence. But wait...there's more.

In collaboration with the O. Press group at University of Washington, the Coulter people have examined the effects of Bexxar therapy with chemotherapy....which we all know we are going to have to do. They described at ASCO, a Phase I/II trial of combining high-dose I131-B1 with chemotherapy (etoposide, cyclophosphamide) and autologous bone marrow transplantation in relapsed patients. Now what this means is as follows....they are going to administer whopping doses of the radioactive material couple to the antibody, and they know it is going to wipe out the bone marrow...and they are going to give very potent and toxic chemotherapy, which they know is also myelosuppressive and they are going to "rescue" these patients from the myeloablative effects of these therapies by reinfusing their bone marrow stem cells that will give rise to new blood cells...and recovery from this massive attack on the lymphoma that will not go away. Very aggressive therapy, but cancer is an aggressive disease. They report treatment ranging up to 850 mCi (contrast that with perhaps 50-75 mCi of single dose administration) calculated to deliver up to nearly 3000 rads to critical organs. Of the 37 evaluable patients (26 with indolent, low-grade lymphoma and 12 with aggressive NHL originally enrolled in study), 33 are alive and 29 are progression free (not necessarily disease free) after 1.5 years. 4 patients have died. This study will continue.

 

In the meantime, the Coulter people have evaluated the with an independent review...the response to B1 antibody therapy in low-grade (or transformed low-grade) NHL...and this is the source of the artistic statistics that Berblady commented on a few days ago, with her astute and discerning fashion. Be that has it may...using the patients that were refractory to further chemotherapy, they examined whether treatment with B1 gave a remission duration or response that was "at least as good" as the last chemotherapy they received...which is an academic question of how are you going to approach treating the refractory patient...and can you do as good as chemotherapy. And wouldn't we rather have anything than chemotherapy, perhaps? But I will not digress at this late stage of information. To make a long analysis short...of the 45 patients evaluated, the question was asked how did they do compared to their last chemotherapy. The facts are: 11 patients did as good with either therapy...19 did better with B1 (at a design cutoff, I believe of at least 1 month median difference) and 11 did better with their last chemotherapy. I will leave it to all the statistic buffs to play with these results...but wait,...

They have at least got the ambition to take on first line therapy, since they now describe two other approaches involving the use of B1. First, there is a recent paper (J. Clin. Oncol. 16: 3270, 1998) in which they report the use again of massive doses of B1 therapy with bone marrow rescue (they purge the bone marrow of potential malignant cells as best they can by a variety of biological techniques) in patients who have relapsed from prior chemotherapy. Hence, this study is like that described above except they don't add the new chemotherapy. The therapy was administered to 29 patients (19 low grade and 10 high grade), most with stage III and IV disease which we would expect. Dosing ranged up to nearly 800 mCi. The results are not easy to interpret (always encounter this with the Press group, but no offense intended)...but as best as I can decipher...25/29 patients responded, and 23 of these were complete responses and the best responses were in the low-grade group (that is as good as I can see for the moment). 11 of 19 patients with indolent lymphoma remain in remission up to about 3-6 years and only 3 of the patients with aggressive disease remain in remission (27, 37 and 87 months). The overall survival rate for low-grade is 78% at 4 years...and the median time to treatment failure is about 3 years for low-grade and about 2 years for the high-grade group.

But it ain't over...they have described a study back at Michigan where this form of therapy has moved to first line with NO prior treatment of any kind in follicular lymphoma, a type that is amenable to this form of therapy (when you analyze all the groups). They received therapy up to the 750 rad limit and the intent is to enroll 60 patients...21 are now evaluable. Complete response in 71% and partial response in 29% (100% total) and of the complete responses, 2 patients have relapsed (median duration not yet reached at about 17 months) and 5 out of the 6 patients who had the partial response have relapsed...and so the intent is to back this treatment philosophy up until limits of success are reached.

 

Oncolym:

Oncolym, interestingly, is the marketed trade name for the radiolabeled Lym-1 antibody when it is ready for infusion...piece of trivia...in contrast to Lym-1 which is the antibody (mouse class IgG2a, originally described by Epstein in 1987 concerning his studies with a monoclonal antibody against an antigen defined on the membrane of a cultured Burkitt lymphoma cell line. This antigen was found to be a mutated form of a Class II recognition antigen (in human systems, called HLA, for Human Leukocyte Antigen)...and specifically, a recognition antigen found on B-lymphocytes (and other cell types) of a subcategory called HLA-DR. These molecules are involved in cell to cell communication and exchange of molecular information regarding the structure of foreign antigens; hence we make immune responses using these recognition molecules. Now, in this lymphoma, this molecule was mutated and Epstein was able to isolate a mouse lymphocyte that makes monoclonal antibodies to it. You can scale up and make a ton of it if necessary and try to treat lymphoma patients if they carried the same molecule on the surface of their B-cell lymphomas (and the rest is history). The best I could track in the literature and I assume there are people familiar with the TCLN message board who go back more than a decade into the beginning of TCLN and may be able to offer more insight into any early studies regarding the use of Lym-1 in therapy of lymphoma, but I could only really track the scientific literature.

 

Most of the published work on Lym-1 comes from the prolific laboratory of the academic group of Sally and Gerald DeNardo at the University of California at Davis. However, there are two major differences that I observed in my reading of the literature on the clinical use of Lym-1 and the literature associated with Bexxar and Rituxan...namely, (1) the lack of apparent funding for the expanded clinical trials needed for Lym-1 as determined by the limited number of trials being conducted and (2) the marvelous scientific methodologies used by the DeNardos in attempts to clearly define the parameters of successful therapy of lymphoma using radiolabeled antibodies. They have set the standard for defining conditions of antibody localization, dosimetry and predictive parameters that help to define exactly who and under what conditions patients will respond to this form of therapy. Will touch on this matter later, just for personal interest. Although published perhaps in only abstract form years ago, some initial therapy was attempted with the “naked” Lym-1 antibody in lymphoma patients, which would be the natural thing to do, since the antibody is of a subtype (IgG2a) that could cause killing of the lymphoma cells under favorable circumstances after binding...but this was not observed. Interestingly, one of the first manuscripts was a case study involving a patient with Ricter’s syndrome, a somewhat bizarre form of chronic lymphocytic leukemia and the patient was nearly moribund with rapidly growing tumor. The patient was successfully treated with a series of infusions with I131-Lym-1 with rapid shrinkage of the tumor sites and the patient was described to be followed over the next 10 months (an average survival for this syndrome was 4 months)...but I have not located (nor searched very hard) a follow-up for this particular patient since the study was an isolated incident published over a decade ago. But it was worthy of historical note, and the initial enthusiasm must have been exciting for the medical staff as well as the family of this patient.

 

Pilot studies in Phase I were taking place before 1987 since one of the first studies was published in 1988 describing treatment of 10 patients with progressive, refractory B-cell malignancies with radiolabeled Lym-1 (everything I write about here involves the use of radiolabeled Lym-1). I will tend to skip through these early studies (1988-1990) rather quickly since the follow-up described in later papers are repetitive and the Phase I studies were examining distribution of antibody, relative uptake at site of tumor compared to normal tissues, etc. Early therapy consisted of fractionated, relatively low doses (25-60 mCi) in intermediate and high-grade patients, almost all with stage III and IV disease, hence the toughest populations of lymphoma patients were being treated...late stage disease, refractory to further chemotherapy and progressive. Of an initial 18 patients, 10 responded (56%, complete or partial) by parameters described in my earlier posts about the Rituxan and Bexxar therapies. Toxicity with these low-doses was modest. However, a brief study published in 1994 described the use of Lym-1 in 5 refractory CLL patients and the use of high-end fractionated doses (up to 65 mCi at 2-6 week intervals) were leading to thrombocytopenia and the group realized that strategies were needed to support this cytopenia before high-dose radiotherapy would be a commonplace modality.

 

Several studies up to the present time from this first definitive study of Lym-1 therapy have focused upon a reevaluation of data already obtained and available while doing Phase I/II studies, such as determining that there is no real reason to exclude patients with splenomegaly (enlarged spleen, usually with tumor burden) from therapy using Lym-1. A paper describing this evaluation of a small subset of patients with splenomegaly was given at the 6th Monoclonal Antibody Conference and also published in Cancer. At the Eleventh International Conference for Use of Monoclonal Antibodies in Cancer, in February of this year, DeNardo presented a paper in the milestones of Lym-1 development, describing in detail their analysis of importance of LDH/KS in determining the response to this therapy (and probably similar therapies under these conditions). In addition, at this meeting, Jamie Oliver described the Phase I/II studies using multidose therapy with Lym-1 in patients with intermediate or high-grade lymphoma. This was co-authored by the DeNardos and carried the byline of Techniclone Corp and USC-Davis. 33 patients with recurrent or refractory intermediate/high grade disease. Doses ranging from 2—200 mCi. Overall, 52% of the patients responded to multidose therapy (CR or PR) with a mean durability of 13 months and those receiving the higher doses had a higher rate of response. Thrombocytopenia is dose-limiting (at about 160-200 mCi). An early report from the multicenter Phase II?III (?) study was also given at this meeting, representing physicians from M.D. Anderson Cancer Center, Cornell Univ., George Washington Med Center, Iowa City VA, and Univ of Miami. Patients enrolled received at least 1 prior chemotherapy and were eligible for up to 4 doses at 160 mCi. 15 patients enrolled, and 9 received at least one therapeutic dose...3 patients with response (1CR and 2PR) and clearly this study is too early to talk about or successfully evaluate...this was earlier this year.

 

This same story was repeated by both sets of authors at ASCO in the spring. For those interested in detailed analysis, the DeNardos published a detailed paper about a year ago in Clinical Cancer Research outlining the analysis of predictive parameters in patients upon which they had a very lot of clinical and laboratory data. Suffice it to say that the development of antimouse antibodies turns out to be a good prognostic factor for ultimate survival time after therapy...i.e., those patients who develop HAMA actually do better...representing some facet of the immune response of these patients not readily apparent in its tie to lymphoma. Two additional items. One, I posted a summary of the recent paper published in Oct describing the value of high-dose, fractionated radiotherapy with Lym-1 and I hesitate to repeat that post here.... (See Post # 181 and 182 to Investor CG). Finally, much of the summary of the therapy involving 88 patients and a description of Phase III studies are given from a description of prior news releases and can be found at:

http://www.wizard.com/NHL/research/Oncolym.htm

 

Relevant References : Sang-Moo, L., et al, Prediction of myelotoxicity using radiation doses to marrow from body, blood and marrow sources. Journal Nuc Med 38:, 1374-, 1997; DeNardo, D.A., et al, Imaging for improved prediction of myelotoxicity after radioimmunotherapy. Sixth Conf on Radioimmunodec and Radioimmunother of Cancer, Suppl to Cancer, ACS, 2558, 1997; Shen, S., et al,, Impact of splenomagaly on therapeutic response and I-131 LYM-1 dosimetry in patients with B-lymphocytic malignancies., ibid, 2553, 1997; DeNardo, et al, Increased survivial associated with radiolabeled Lym-1 therapy for non-Hodgkin's lymphoma and chronic lymphocytic leukemia., ibid, 2706, 1997; DeNardo, G.L., et al., Overview of radiation myelotoxicity secondary to radioimmunotherapy using I131-Lym-1 as a model Cancer, 73:, 1038-, 1994.; DeNardo, S.J., et al. A direct apporach for determining marrow radiation from MoAb therapy, in Biology of Radionuclide Therapy, Washington, DC, Amer Coll Nuc Phys, , 110, 1989; DeNardo, G.L., et al, Body and blood clearance and marrow radiation dose of I131-Lym-1 in patients with B-cell malignancies. Nucl Med Commun, 14: 587-, 1993.

 

11/22/1998

With respect to the article published this past month by the DeNardo's (J Clin Oncol 16: 3246, 1998), it was asked whether this is "old" or "new" data, with inflection, I assume on whether these terms represent progress in the company's trials for this product. All published data is rather "old" due to the lag in publication time found for academia and clinical results always represent a follow-up period of substantial length due to the nature of the disease in its time of remission or ultimate progression. I prefer to look at the data in this article as a natural extension of PhaseI/II studies designed to optimize the parameters by which they can administer the highest possible radiation dose to the site of lymphoma and maintain acceptable toxicity. This study defined the ability to "fractionate" the total radiation delivered into separate infusions of labeled antibody (about 4 weeks apart, up to 4 doses, but most received two therapeutic doses). All patients, as usual, were refractory to further chemotherapy and all grades (low, intermediate and high) of NHL were included. Several objective results were found and can be summarized in my ususal simplistic manner: (1) if you do NOT respond to radiolabeled antibody therapy, you are in big trouble and will succumb quickly to progressive disease, (2) of the 21 "entries" (1 patient entered the trial twice) into this analysis, about 50% of the patients were responders (33% complete) and the best overall response was observed with the low-grade NHL (in terms of survival and duration of remission) although half of the intermediate and high-grade patients also responded to this therapy, and (3) if you are able to achieve high-dose delivery (about 200mCi per patient), the response rate approaches 100%.

 

This publication does define what can be accomplished in terms of maximum dose delivery and value of fractionating the radiation. This information, together with the knowledge of toxicities carefully outline the nature of how clinical treatment with this agent is packaged for Phase III trials. However, what remains to be determined with Lym-1 is how quickly the studies can be pushed to front-line status, in the following sense: (1) DeNardo mentions that it is likely that patients can respond to repetitive rounds of Lym-1 therapy since relapsed patients retain expression of the Lym-1 antigen, which is encouraging. This is being done by the Bexxar group (using the CD20 antigen) and there has been considerable discussion regarding this strategy in light of the short responses (or none) to continued chemotherapy (or different chemotherapy) by M. Winn, BobLLL and Berblady that has been interesting and quite informative. (2) How does one start needed studies on combination therapy (chemo + Lym-1) and what is the optimal schedule, dose and timing of that form of therapy? Finally, how does one put together an informative, knowledgeable and meaningful discussion of comparing Bexxar, Rituxan and Lym-1 together? It is extremely tedious and laborious to sort out the nuances of the clinical studies of different groups.

 

Interesting clinical case study that outlines in detail how therapy with Oncolym goes in the clinic. As brief as I can make it...patient diagnosed in 1985 with NHL, underwent 6 cycles of CHOP chemo to complete remission...relapse in 1986...another year or so on chlorambucil and prednisone...poor reponse then progression...9 cm scalp mass, cervical node involvement...occipital mass, etc. May, 1988, underwent three courses of Lym-1 with progressive shrinkage of masses...(quickly developed human anti-mouse antibodies, HAMA, final comment on this later)...Jan, 1989 had two rounds of localized radiation therapy to resolve sclertotic abnormality on skull x-ray...went 7 years with no evidence of disease...recurred in abdomen in Dec 96. Tough disease, aggressive therapy name of the game). Couple of interesting clinical points. Within one month of initial Lym-1 treatment, patient had high titer of HAMA (which may preclude further therapy with mouse antibodies in some instances...but "humanized" antibody hybrid molecules are overcoming that...)...but they manipulated the plasma levels of HAMA sufficiently to have three cycles of Lym-1 treatment. What was of interest...besides the patient making an immune response against the mouse antibody (Lym-1)...the patient also made antibodies against the targeting sequence of the Lym-1...in other words...an additonal family of antibodies that may have actually helped in targeting lymphoma cells. This may have also been a factor in the 7-year disease free interval. For those who want to appreciate the clinical course of NHL and therapy...this article reads easily, and is found in Cancer Biotherapy & Radiopharmaceuticals 13: 1-12, 1998, entitled, "Prolonged survival associated with immune response in a patient treated with Lym-1 mouse monoclonal antibody", by SJ Denardo, et al.

 

12/28/1998

Maximum-Tolerated Dose, Toxicity, and Efficacy of 131I-Lym-1 Antibody for Fractionated Radioimmunotherapy of Non-Hodgkin's Lymphoma
By Gerald L. DeNardo, Sally J. DeNardo, Desiree S. Goldstein, Linda A. Kroger, Kathleen R.
Lamborn, Norman B. Levy, John P. McGahan, Qansy Salako, Sui Shen, and Jerry P. Lewis
Purpose: Lym-1, a monoclonal antibody that preferentially targets malignant lymphocytes, has induced remissions in patients with non-Hodgkin's lymphoma (NHL) when labeled with iodine 131(131I). Based on the strategy of fractionating the total dose, this study was designed to define the
maximum-tolerated dose (MTD) and efficacy of the first two, of a maximum of four, doses of 131I-Lym-1 given 4 weeks apart. Additionally, toxicity and radiation dosimetry were assessed.
Materials and Methods: Twenty patients with advanced NHL entered the study a total of 21 times. Thirteen (62%) of the 21 entries had diffuse large-cell histologies. All patients had disease resistant to standard therapy and had received a mean of four chemotherapy regimens. 131I-Lym-1 was given after Lym-1 and 131I was escalated in cohorts of patients from 40 to 100 mCi (1.5 to 3.7 GBq)/m2 body surface area.
Results: Mean radiation dose to the bone marrow from body and blood 131I was 0.34 (range, 0.16 to 0.63) rad/mCi (0.09 mGy/MBq; range, 0.04 to 0.17 mGy/MBq). Dose-limiting toxicity was grade 3 to 4 thrombocytopenia with an MTD of 100 mCi/m2 (3.7 GBq/m2) for each of the first two doses of 131I-Lym-1 given 4 weeks apart. Nonhematologic toxicities did not exceed grade 2 except for one instance of grade 3 hypotension. Ten (71%) of 14 entries who received at least two doses of 131I-Lym-1 therapy and 11 (52%) of 21 total entries responded. Seven of the responses were complete, with a mean duration of 14 months. All three entries in the 100 mCi/m2 (3.7 MBq/m2) cohort had complete remissions (CRs). All responders had at least a partial remission (PR) after the first therapy dose of 131I-Lym-1.
Conclusion: 131I-Lym-1 induced durable remissions in patients with NHL resistant to chemotherapy and was associated with acceptable toxicity. The nonmyeloablative MTD for each of the first two doses of 131I-Lym-1 was 100 mCi/m2 (total, 200 mCi/m2) (3.7 GBq/m2; total, 7.4 GBq/m2).

J Clin Oncol 16:3246-3256.

Address reprint requests to Gerald L. DeNardo, MD, Molecular Cancer Institute, 1508 Alhambra
Blvd, Room 3100, Sacramento, CA 95816; Email [email protected].

 

Interesting correspondence (J. Clin. Oncol. 16: 3916, 1998): We have discussed before the theoretical possibility that sustained treatment with antiCD20 (and presumably other antigen directed antibody approaches) could eventually select for the emergence of a subpopulation of lymphoma cells that would be negative for the expressed intact CD20 antigen target molecule. Such a case has been reported (cited above). Japanese group report that 5 months after Rituximab antibody therapy, relapse with lymphoma-positive bone marrow revealed variant lymphoma population that was CD20, presumably precluding further therapy with Rituximab. This has been reported before (J. Clin. Oncol. 16: 1635, 1998). Interestingly, when one speaks of retreatment of patients and an overall 40% response rate...about half of the patients do not respond (due to unknown mechanisms). Now, this report leads to a clue, i.e., a reduction, mutation, or loss of the target antigen on the relapse lymphoma cells. Certainly, this could happen with Lym-1 also, but I do not know of retreatment data at the present time. Theory in biology usually means it will happen, given enough observations...

 

01/05/1999

Provided by a colleague: (edited), filed on UPI under Health Notes.NEW BRAIN CANCER THERAPY: Each year, 15,000 Americans are diagnosed with terminal brain cancer. Now, there's a glimmer of hope for some of them, thanks to a new targeting agent called Tumor Necrosis Therapy. Developed by Techniclone Corp. and undergoing Phase II human clinical trials, the therapy allows doctors to deliver high concentrations of radiation directly to the tumor's core through the use of a low-pressure intra-tumoral catheter, essentially killing the tumor from the inside out while potentially causing no damage to healthy surrounding tissue and with minimal adverse side effects. Of the six malignant glioma brain tumor patients who underwent Phase I trials, all showed stabilization of the tumor and three actually had tumors that shrank despite receiving doses that were 1/3 to 1/2 of what is considered to be an effective dose to treat this disease. In the past, victims diagnosed with this form of brain cancer were faced with two treatment options, both of which have proven ineffective over the long term. If the tumor is operable, doctors are only able to remove the bulk of the tumor, leaving behind microscopic ``tentacles'' which ultimately results in re-growth. External treatments such as radiation and chemotherapy have always been limited in their effectiveness, since doses are regulated in order to minimize damage to the surrounding brain tissue. TNT, however, may prove in clinical trials to severally reduce the amount of toxic agents necessary to kill the tumor by directly targeting its core, says Larry Bymaster, Techniclone's CEO. ___ By LIDIA WASOWICZ - UPI Science Writer=

 

01/08/1999

This is a remarkable document. Thorpe is a first-class scientist. While I understand the science contained within the granted patent, I am unable to entirely grasp the protection it may afford TCLN regarding this type of methodology. It is important to discern between what might be argued as comprehensive in a scientific discussion and what may be argued in a legal battle over patent rights regarding the delivery of reagents to a targeted vascular bed of blood vessels within a tumor. Hence, I am not able to speak of what could be challenged or undone. However, in my opinion, if one contemplates the delivery of nearly any reagent used in the diagnosis, imaging or therapy of a vascularized tumor by an antibody-based technology, no matter the form that antibody may be constructed (genetically engineered or produced monoclonal, or even induced polyclonal); then Thorpe's patent has it covered. No matter the target antigen on the endothelial cell that at least I can envision, if one wants to target that molecule (assuming that it is preferentially displayed in tumor endothelium), then the patent has it covered. It is comprehensive and complete in that respect. In lay terms, the delivery of any agent via an antibody construct to tumor blood vessels belongs to TCLN according to how I read the granted claims of this patent. It seems straight-forward. TCLN knows how to write a patent.

 

Now, what does this mean in the world of anti-angiogenesis (the ability to prevent or eradicate the blood supply of a growing tumor)? The inhibition of endothelial cell division, or migration of those cells, or their ability to form proper tubules within a tumor would inhibit tumor growth. Hence, regarding these properties, there may be several expressed properties and receptors of endothelial cells that could be exploited as therapeutic targets. The most obvious and well-known molecules, angiostatin and endostatin (ENMD) inhibit the growth of endothelium by a manner not entirely characterized, but these molecules are not delivered to the blood vessels by antibody or similar vehicles, hence they remain outside the scope of this patent in my opinion. Not addressed in this patent is the targeting of the well-known VEGF-receptor being addressed by companies such as Genentech or Chiron, but small molecular-weight compounds that target the enzymatic properties of this receptor would seem not to fall inside this patent. In other words, the world of anti-angiogenesis is filled with companies attempting to evaluate new kinds of molecules that have specific molecular targets and these molecules are NOT delivered by immunologically-based devices, such as antibodies or antibody-constructs. Examples include angiostatin-endostain fusion protein (Genetix); combretastatinA4 (OxiGene), Flt-1 soluble receptor (Merck); Kringle5 (Abbot); 2-methoxy-estradiol (ENMD), carbohydrate-RG8803 (Repligen); PD-173074 kinase inhibitor (Parke-Davis); S-836, a integrin antagonist(Monsanto); small molecular antagonists, TBC series (Tex Biotech Cor); Angiozyme, a catalytic destroyer of VEGF-receptor RNA (Ribozyme Pharma); NX1838 antagonist of VEGF (Nexstar); SU5416, an inhibitor of the VEGF-receptor (Sugen); ZD101, an endotoxin that may stimulate an immune response against blood vessels (Zeneca); AG3340, a matrix enzyme inhibitor (Agouron, Phase III); Marimastat, similar inhibitor (Brit Biotech, Phase III);...and on and on. Many of these molecules have not yet made it into clinical trials. But the list of compounds being synthesized and evaluted in preclinical animal studies is growing. However, the antibodies against the VEGF-receptor and cadherins being pursued by ImClone could be sticky with respect to this patent. But that's for lawyers.

 

Finally, outside of the scope of this patent are approaches championed by Ruoslahti who demonstrated in a series of elegant studies the ability to select phage (bacterial viruses) that preferentially bind to endothelium in tumor sites and has used these phage with attached drugs to kill tumors in mice. There are efforts to construct peptides with particular amino acid sequences (kind of a combination biochemistry synthetic antibody-type molecule) that bind to target molecules on endothelial cells and these peptides could be argued not to be of an immunological delivery system, i.e., not fashioned using variable regions of immunoglobulin genes. In addition, there are a number of studies attempting viral-mediated delivery of genes and reagents to endothelium that could be argued to fall outside the scope of this patent, in my opinion. Certainly Thorpe has done a magnificent job with his studies, and the scope of this patent with respect to protection of the VTA technology as envisioned by TCLN. Remember, everything I have said is pure academic opinion which is a lot different than business-based competition or the currency of lawyers.

regards.

 

01/09/1999

Cancer Treatments

Gee, doccg, you are a brave person to ask me about expressing my views on an approach to cancer treatment. Let me extend that question to an excuse to give the following views:

Malignant disease: Cancer is a collection of heterogeneous diseases that follows an unchecked genetic, and heritable change in the DNA of a single cell that results in unregulated proliferation of that cell and its daughters until the mass/metabolism of the primary tumor or its metastasis shuts down normal function of vital organs resulting in death. The cancerous changes that occur (e.g., leukemias; immune cells; sarcomas, of connective tissue and bone; carcinomas, the common solid tumors of gastric, colon, kidney, liver, breast, prostate) may be unique to the tissue type and perhaps to the genetic susceptibility of the individual. For example, loss of the p53 suppressor gene (the normal function of this gene is to regulate just how many times a cell can undergo cell division without being called into question about its motives for continually dividing) is known to occur in about 40-50% of carcinomas that are aggressive, highly metastatic, autonomous from tissue regulation and deadly. Other examples of “suppressor” genes include for instance, the retinoblastoma gene, RB, the breast cancer set, BRCA1 and 2; and other less common or mentioned genes. Of course, on the other side of the coin is the activation of tumor-inducing genes (which functionally inactivate suppressor genes), which can occur by genetic alteration of environmental insults (tobacco carcinogens, hydrocarbon-damage, UV induced damage, etc). Suffice it to say, once the malignant transformation of a single cell occurs, forces are set into motion that determine the destiny of the patient...does that cell survive which such …  (?message truncated?)

 

Therapies: Everything is based upon the premise that cancer cells have metabolic properties that are unique or abundant compared to normal tissue and therefore are more sensitive to toxic agents designed to kill dividing cells. Name of the game. Kill dividing cells. Kill relatively more cancer cells than normal cells. Over the past 3 decades, most chemotherapeutic regimens have been based upon exploiting natural biochemical pathways known to be essential to dividing cells and are somewhat sensitive in tumor cells. That’s why chemotherapy is eventually limited by normal cell toxicity (GI tract, bone marrow; neuronal); our natural need to replenish vital cell populations involved in the everyday housekeeping functions of our body and maintain normal cell function (platelets, leukocytes, mucosal cells of the GI tract, functions of neurons) ultimately limit our ability to poison our bodies with drugs designed to kill anybody that’s moving. Hence, for purposes of this discussion, chemotherapy will always fail. Always. Why?

1. Because drug-limiting toxicity is of normal tissue, not cancer.
2. Because the pressure of drug administration always selects drug-resistant cells out, even though this phenomenon is highly sensitive to variables of dose and schedule in the administration of drug.
3. There are sites that harbor tumor cells that may not allow penetration or proper metabolism of the chemotherapeutic drug, thereby sparing dormant tumor.

Therefore, the continued search for toxic agents is starting to require very stringent conditions in order to improve upon our toxic therapy available today. Let me explain. If you discovered a compound that interfered with DNA synthesis in a very simple way (say, inhibition of a required, though boring enzyme), chances are your therapy of cancer with that compound would quickly reach unmanageable doses because even the normal cells that divide in our body require that everyday, boring enzyme, therefore, your new drug is not very effective; because it did not have a “therapeutic index” of being more important to the cancer cell than the normal cell. That’s why. Trust me. I am eventually getting to your question, doc.

Modern “chemotherapy” is attempting to exploit specific metabolic pathways that may be very, very sensitive and required and relied upon by cancer cells; yes, these pathways are found in normal cells, but not to the same sensitivity. The tumor may have left itself vulnerable, because it needed to synthesize more of a particular enzyme, or express more of a certain receptor than its corresponding normal cell in order to metastasize to a particular organ and survive (remember, the cancer cell is always “out of place”; a feature to mention later). Therefore, new medicinal chemistry of cancer is very much centered upon inhibition of over-expressed molecules (figuring that if the cancer cell didn’t need so many of these proteins, they wouldn’t express so many). Turns out these overexpressed proteins are very important to continued proliferation by the cancer cells, the so-called growth factor receptors, the kinases, the enzyme machinery of rapidly dividing cells, they are now the targets of the new “molecular therapy”. These inhibitors are in clinical trials; they do not have quite the classical toxicity of ragged chemotherapy, but we need to see if they can eradicate the tumor. What new molecular tricks will tumor cells play to always produce a progeny capable of circumventing the ability of us to turn off their vital pathways. There will be alternate pathways the cells will invoke (select for daughter cells that have this property); or inactivation pathways of our targeting agent...etc. We just don’t really know yet.

 

Eradication of cancer (theory): The stuff of ordinary, but very bright research people at the bench that have little interest in the stock market, but just do good and imaginative work everyday. Well, you can carry the comments of chemotherapy into radiation therapy very quickly and come to similar conclusions. Radiation therapy (external beam of photons or particles) has deleterious side effects that eventually render this modality of suspect effectiveness. I have also mentioned several times over the past months about the possibility that toxic drugs and radiation delivered by targeted vehicles (such as antibody; Rituxan, Bexxar, lym-1) can be eventually limited by the expression of the target antigen by malignant cells, or the penetration of these agents into privileged areas of the body that may harbor cancer cells but not allow entrance of large molecular weight antibodies. I am particularly enamored by the delivery of molecules to the vicinity of the tumor by the TNT-generation of antibodies and fusion peptides for reasons thoroughly discussed before; because of the exploitation of a natural necrosis that occurs in the vicinity of a rapidly growing tumor mass by the TNT targeting and the ability of such targeting to induce inflammatory changes that, in my opinion, are favorable to subsequent host defense responses against the tumor.

In my opinion, based upon my experience in preclinical studies of cancer, curative procedures will only be obtained by ultimate recognition of the malignant cell by a competent immune system capable of mounting an effective immune response against the neoplasm, or by systemic initiation of a cessation of cell division and induction of a terminal differentiation of cancer cells, who have suddenly been induced to realize that they are part of a programmed tissue that no longer needs to divide. I see no other potential therapeutic interventions that can achieve permanent regression of malignant tissue. The first modality, immunotherapy, has been attempted in cancer for over 30 years with very limited success and we are coming to realize that the differences we have been looking for (the BIG foreign antigen that makes the cancer cell an immunological monster easily recognized and eradicated) are not there...the changes are very subtle, but perhaps noticeable. As our knowledge of classical immunology expands, (especially transplantation immunology, our creative juices in the area of cancer immunology improves). There are several viable approaches today that are very promising. The second property, that of programmed normal behavior is rapidly evolving...and in an interesting fashion. Gene therapy is actually based upon the premise that one can somehow restore normal cell function to the cancer cell by replacing the known defective genetic elements that have gone astray (say, that p53 gene mentioned earlier; put in a new one!). Yet, it is tough to imagine how we are gonna deliver genes to big tumor masses or scattered small metastases throughout the body. There are thoughts, but no concrete or convincing approaches to that yet. We can envision agents that induce new pathways, kind of an embryo-approach...that says to the cancer cell, picture yourself as a liver cell, or colon cell, or well-behaved lung cell, please. The cells stop dividing, become quiescent and as mannered as a boarding-school freshman.

 

02/03/1999

Fusion peptides: Need to discuss some properties of two cytokines; interleukin-2 (IL-2) and interferon-gamma (FN-g), which are molecules released by lymphocytes that have a myriad of immune-stimulating properties and are very important in antitumor responses. IL-2 has been used (with modest success) in a variety of cancers, but has a deleterious side effect that limits its use, namely, vascular-leak syndrome, where leakage of the vascular compartment takes place into tissues. This is because IL-2 causes an increase in the permeability of endothelial cells to water (either by direct or indirect mechanisms); and this syndrome is life-threatening. IFN-g activates a variety of immune cells which aids in antitumor activity and also causes tumor cells (and other immune cells) to express new levels of needed cell-surface molecules that assist in destruction of tumor. Now, one other facet of this strategy must be mentioned, the TNT antibody molecule; which is an antibody directed to nuclear antigens found in necrotic regions of growing tumor and is the basis of TNT-therapy with which we are familiar.

 

Epstein has taken advantage of the exquisite localization of TNT antibody to the region of tumor by considering also the local delivery of IL-2 or IFN-g and at the same time, exploited that side effect of IL-2, i.e., its effect on local permeability of endothelial cells. Now, antibodies are formed by the linking of several protein molecules due to gene rearrangement prior to their synthesis. The antibodies are secreted by lymphocytes and this synthesis of the TNT antibody (to which the isotope I-131 can be added is toxic to cells in the vicinity of its binding, like in treatment of glioma) can be duplicated in the laboratory in expression systems that artificially make tons of antibody of against a specific target. Hence, the TNT therapy machine. However, by genetic engineering, we can take the molecular targeting of the TNT antibody (to vicinity of tumor) and hook up genes that will also attach the IL-2 (or IFN-g) molecule directly to the antibody. Now we have one antibody-interleukin protein, a so-called fusion peptide, since it is due to the “fusion” of two distinct gene-products normally not related.

 

Epstein now proposes (and he has good funding for these projects) to synthesize these fusion-peptides to cause localized changes in the tumor microenvironment that will aid in other types of therapies. The I-131 is no longer attached. For example, the TNT/IL-2 constructed peptide will cause localized permeability changes in the vicinity of the tumor and allow easier delivery of other agents that might have a tough time penetrating the blood vessels (endothelial cells) to get inside the tumor mass. These agents might include chemotherapeutic drugs normally used in cancer therapy or larger molecules, such as other types of antibodies or related agents. On the other hand, the fusion-peptide containing IFN-g may allow localized upregulation of antigens on cells that aid in immune responses. Only the creative imagination of the scientist in this setting limits the possibilities of new types of therapeutic approaches using fusion-peptides of different constructs. This is the essence of this technology and I view it as imaginative (Epstein is a very gifted scientist) and filled with possible new treatment regimens. Of course, the test is in the clinic. But he has published about preclinical models. When I have time I can post some of those references.

 

02/03/1999

The TNT antibody currently in use for glioma (and I suppose the Mexico trials in other solid tumors) uses an attached radioactive isotope, I-131 as the source of toxicity to the tumor cells. The antibody attaches to the displayed antigens offered by the tumor region, and the accompanying radiation kills tumor cells within that region. Now, you may be confusing the use of Oncolym (which is an antibody also containing the radioactive isotope used against a lymphoma antigen in NHL), and Rituxan, the IDEC antibody against lymphoma cells which does not carry a radioactive molecules attached to it, because it can mediate tumor cell destruction by a different mechanism. TNT antibody and Oncolym antibody are two different antibodies against two different target antigens found on different tumors.

chTNT-3 (next generation) can be used to deliver a variety of attache goodies...kind of in a payload fashion, with the docking end the antibody that recognizes the good ole TNT antigen. Not related to patent, since it is not directed to endothelial cell antigens...(without getting into complex legal interpretations).

Epstein just used the radioactive thymidine molecule as a tracking drug to show that IF he had used real chemotherapeutic drug (the thymidine was just used in a radioactive fashion so he could show how it was taken up in tissue)then the use of the chTNT enhanced uptake of the drug by about 3-fold.

Hope this was helpful...

 

02/03/1999

Pretreatment with a monoclonal antibody/interleukin-2 fusion protein directed against DNA enhances the delivery of therapeutic molecules to solid tumors. Clin Can Res 1999
Hornick JL, Khawli LA, Hu P, Sharifi J, Khanna C, Epstein AL
Department of Pathology, University of Southern California School of Medicine, Los Angeles 90033, USA.
[Medline record in process]
The efficacy of molecular therapies for human malignancies is limited by inadequate accumulation within solid tumors. Our laboratory has developed a novel approach that uses monoclonal antibodies (MAbs) to direct vasoactive proteins to tumor sites to increase local vascular permeability and, in turn, improve the delivery of therapeutic reagents. Previously, we demonstrated that pretreatment with immunoconjugates containing interleukin-2 (IL-2) enhances specific tumor uptake of radiolabeled MAbs without affecting normal tissues. In the present study, we describe a fusion protein consisting of a chimeric antinuclear antibody and IL-2 (chTNT-3/IL-2) and illustrate its potential for improving the delivery of both MAbs and drugs. The ability of pretreatment with chTNT-3/IL-2 to increase specific tumor uptake of the MAb B72.3 was demonstrated in LS174T colon tumor-bearing mice. Tumor accretion of B72.3 increased nearly 3-fold, with no changes in normal tissues. Abrogation of this effect with N(G)-methyl-1-arginine, a chemical inhibitor of nitric oxide synthase, suggests that rapid generation of nitric oxide in the tumor is responsible for the enhanced uptake. To demonstrate that pretreatment with chTNT-3/IL-2 can improve the uptake of other clinically relevant MAbs in different tumor models, additional studies were performed in both lung and prostate xenograft models. Pretreatment with the fusion protein increased specific tumor uptake of the MAb NR-LU-10 in A427 lung tumor-bearing mice and enhanced tumor uptake of the MAb CYT-351 in LNCaP prostate tumor-bearing mice, 2.1-fold and 1.7-fold, respectively. Finally, tumor uptake of the radiolabeled thymidine analogue 125IUdR also increased approximately 3-fold after pretreatment, indicating that this approach can be extended to small molecules such as chemotherapeutic drugs. Because TNT-3 recognizes a universal nuclear antigen accessible in degenerating and necrotic cells within all solid tumors, this strategy may be applicable to the majority of human cancers.

 

02/05/1999

I have mentioned that one of the strengths of the DeNardo's is their incessant penchant for refining methodologies associated with radioimmunotherapy with monoclonal antibodies. This recent paper (Dec)demonstrates their interest and potential use of yittrium-labeled Lym-1 by use of new methodology. Productive and cost-effective...good biotech terms. This paper is of limited clinical interest to readers here, but I offer it as evidence that DeNardos and the lym-business goes on...

J Nucl Med 1998 Dec;39(12):2105-10

Optimized conditions for chelation of yttrium-90-DOTA immunoconjugates.

Kukis DL, DeNardo SJ, DeNardo GL, O'Donnell RT, Meares CF
Department of Internal Medicine, University of California Davis Medical Center, Sacramento, USA.

Radioimmunotherapy (RIT) with 90Y-labeled immunoconjugates has shown promise in clinical trials. The macrocyclic chelating agent 1,4,7,10-tetraazacyclododecane-N,N',N",N"'-tetraacetic acid (DOTA) binds 90Y with extraordinary stability, minimizing the toxicity of 90Y-DOTA immunoconjugates arising from loss of 90Y to bone. However, reported 90Y-DOTA immunoconjugate product yields have been typically only < or =50%. Improved yields are needed for RIT with 90Y-DOTA immunoconjugates to be practical. METHODS: (S) 2-[p-(bromoacetamido)benzyl]-DOTA (BAD) was conjugated to the monoclonal antibody Lym-1 via 2-iminothiolane (2IT). The immunoconjugate product, 2IT-BAD-Lym-1, was labeled in excess yttrium in various buffers over a range of concentrations and pH. Kinetic studies were performed in selected buffers to estimate radiolabeling reaction times under prospective radiopharmacy labeling conditions. The effect of temperature on reaction kinetics was examined. Optimal radiolabeling conditions were identified and used in eight radiolabeling experiments with 2IT-BAD-Lym-1 and a second immunoconjugate, DOTA-peptide-chimeric L6, with 248-492 MBq (6.7-13.3 mCi) of 90Y. RESULTS: Ammonium acetate buffer (0.5 M) was associated with the highest uptake of yttrium. On the basis of kinetic data, the time required to chelate 94% of 90Y (four half-times) under prospective radiopharmacy labeling conditions in 0.5 M ammonium acetate was 17-148 min at pH 6.5, but it was only 1-10 min at pH 7.5. Raising the reaction temperature from 25 degrees C to 37 degrees C markedly increased the chelation rate. Optimal radiolabeling conditions were identified as: 30-min reaction time, 0.5 M ammonium acetate buffer, pH 7-7.5 and 37 degrees C. In eight labeling experiments under optimal conditions, a mean product yield (+/- s.d.) of 91%+/-8% was achieved, comparable to iodination yields. The specific activity of final products was 74-130 MBq (2.0-3.5 mCi) of 90Y per mg of monoclonal antibody. The immunoreactivity of 90Y-labeled immunoconjugates was 100%+/-11%. CONCLUSION: The optimization of 90Y-DOTA chelation conditions represents an important advance in 90Y RIT because it facilitates the dependable and cost-effective preparation of 90Y-DOTA pharmaceuticals.

 

TNT

Interesting case study presented 4 years ago at ASCO.

Response of hormonally refractory prostate cancer (HRPC) to TNT-1 monoclonal
antibody (Meeting abstract).

Proc Annu Meet Am Soc Clin Oncol. 13:A742, 1994.

Abstract
Treatment options for HRPC are severely limited with responses to current chemotherapy regimens usually being of short duration. TNT-1 is a murine monoclonal antibody which has been shown to bind specifically to degenerating and dead cells of human cancers (Epstein et al, Cancer Res 48:5842-8, 1988). The antibody recognizes an antigenic domain of nuclear histones which is expressed in all cancers and normal tissues studied to date. Inadequate blood supply and impaired phagocytic responses within the tumor favor the accumulation of degenerating cells adjacent to viable areas of the tumor. In contrast, normal tissues have a relatively low rate of cell death and are characterized by a rapid and orderly removal of necrotic elements. We report successful treatment with TNT-1 MoAb in a 47 year old man with HRPC with prior treatment that included orchiectomy, flutamide, suramin, radiation therapy and doxorubicin. Within 36 days after the administration of 50 mg of biotinylated TNT-1 followed by 20 millicuries of 131I-streptavidin given weekly times 2, the PSA declined from 210 to 4.9 and the PAP from 6.5 to 1.2. The patient was clinically improved and remained stable for 10 months having received only TNT-1 for 2 such treatment cycles. Moderate thrombocytopenia and leukopenia with nadirs at day 36 after treatment were noted. Further clinical evaluation of TNT-1 against a broad spectrum of tumor types is now being considered. (C) American Society of Clinical Oncology 1997

 

Granted, we are not out of the first generation TNT clinical studies, but looking ahead is always a good distraction. Epstein published a paper last year (Radiochemica Acta 79: 83-86, 1997) on initial preclinical studies using TNT-IL2, the often mentioned fusion peptide construct. As we know, TNT is an antibody that targets specific DNA-associated proteins within necrotic regions of tumor, and this target rarely, if ever, mutates as do other molecules of cancer cells, thus making these proteins valuable for docking onto and delivering toxic molecules to the microenvironment of cancer. The fusion construct is the antibody genetically combined with an active cytokine, called IL2, which has two major effects (1) promotes activation and receptor expression of immune cells against tumor and (2) causes tremendous increase in local permeability of blood vessels allowing blood-borne molecues to infiltrate the tumor. Hence, targeting the TNT-IL2 molecule to tumor causes the uptake of drugs to be increased about 4-fold over the use of a placebo antibody...and significantly improves the therapeutic index while causing no increase in toxicity or uptake in normal tissues over that observed as normal. More delivery to tumor. This approach is where the next ideas will be carried out...and represents further potential value in the product platform of TCLN,

 

TNT mAb is directed against a nucleohistone antigen exposed in degenerating cells; and the past and ongoing literature is contained in (a) Hornick, et al, A chimeric TNT/IL-2 antibody fusion protein as a universal pretreatment to enhance the delivery of therapeutic molecules to solid tumors, ProcAACR, 1997; (b) Khawli, et al, Effect of seven new vasoactive immunoconjugates on the enhancement of monoclonal antibody uptake in tumors, Cancer 73:, 1994; (c) Khawli, et al, Chemical modification of monoclonal antibodies; ProcAACR, 1994; (d) Khawli, et al, Enhancement of chemotherapetuic index by a monoclonal antibody vasoconjugate, ProcAACR, 1994; (e) Strum, et al, Response of hormonally refractory prostate cancer (HRPC) to TNT-1 monoclonal antibody; ProcASCO, 1994; (f) Miller, et al, Immunolgoci and biochemical analysis of TNT-1 and TNT-2 monoclonal antibody binding to histones; Hybridoma 12:, 1993, (f) Epstein, et al, Tumor necrosis treatment of human cancers; ProcAACR, 1992; (g) Chen, et al, Effects of 131-I-labeled TNT-1 radioimmunotherapy on HT-29 human colon adenocarcinoma spheroids, Can Immunol Immunother, 33:, 1991; (h) Gaffar, et al, Cell based radioimmunoassays to quantitate the immunoreactivity of TNT monoclonal antibodies directed against intracellular antigens, J. Immuno 12:, 1991; (h) Cheng, et al, Diffusion and binding of monoclonal antibody TNT-1 in multicellular tumor spheroids J. Natl Cancer Inst 83:, 1991, (i) Chen, et al, Localization of monoclonal antibody TNT-1 in experimental kidney infarction of the mouse, FASEB J 4:, 1990; (j) Chen, et al, A comparative autoradiographic study demonstrating differential intratumor localization of monoclonal antibodies to cell surface (Lym -1) and intracellular (TNT-1) antigens, J Nucl Med 31:, 1990; (k) Chen, et al, Tumor necrosis treatment of ME-180 human cervical carcinoma model with 131-I-labeled TNT-1 monoclonal antibody, Cancer Res 49:, 1989

 

An encouraging aspect of the TNT Phase I studies being done at South Carolina is that these studies will be shifted to Phase II involving 4 medical centers (probably including M. Berger's department at UCSF). Recalling the news release of Oct 1 (which tend to get lost), TCLN will recruit 1/2 of the patients that have newly diagnosed glioblastoma or anaplastic astrocytoma and the other half from patients with recurrent disease (it almost always recurs). Dosage will be individualized to each patient, (two doses, 8 weeks apart). Phase II endpoints are efficacy (response) as determined by stabilization of disease and time to disease progression as well as continued study on safety and tolerability. Remember, they noted antitumor responses in all of the initial Phase I patients, even at low doses...but I have not heard any follow up on those patients. Whether Patel found a way to make it to the program of the Neuro-Oncology meeting is unknown at this time...but the secretary of the meeting is here at the Tex Med Center, I will try to contact her and found out more.

 

VEA

December 9, 1996 -- Techniclone Corporation (NASDAQ: TCLN), a biotechnology company engaged in the research and development of drug delivery systems based on monoclonal antibodies announced today that a team of scientists from the University of Southern California and the Mayo Clinic have published an article discussing the combined use of Techniclone’s patented LYM-1 and Vasopermeation Enhancement in preclinical (animal) studies. The Company’s Director of Scientific Affairs, Alan L. Epstein, M.D. Ph.D. and Peter M. Anderson, a member of Techniclone’s Scientific Advisory Board, were part of the group who published the article.

The article, published in Cancer Research, November 1, 1996, indicated that Vasopermeation Enhancement technology and administered as a pretreatment, enhanced the uptake of radiolabeled LYM-1 antibody specifically in the tumor by an average of 300%. They concluded that Vasopermeation Enhancement increased the tumor’s permeability, suggesting that this combination may be a new form of therapy which could be used in humans.

Authors of the article include Peishing Hu, Jason L. Hornick, Michelle S. Glasky, Aoyun Yun, Mary N. Milkie, Leslie A. Khawli, and Alan L. Epstein, all of the University of Southern California Department of Pathology, and Peter M. Anderson of the Mayo Clinic Section of Pediatric Hematology/Oncology.

"This new fusion molecule utilizing our Vasopermeation Enhancement technology appears to be several times more effective than LYM-1 alone (presently in Phase III clinical trials), and reflects the efforts of our scientists to continuously test and improve the Company’s product pipeline" said CEO Lon H. Stone.

 

02/05/1999

At the risk of turning this forum into a library, we have discussed the next generation TNT molecues, i.e., the fusion peptides, where cytokines or advantageous molecules are genetically linked into the formation of the TNT antibody. Here is an older paper that describes early work by Epstein a fusion-peptide with the LYM-1 antibody, the basis of current Oncolym therapy for NHL.

It does show one that if sufficient funding were available, and clinical trials are extremely expensive; it would be very interesting to pursue these kind of "hidden" pipeline methodologies, that probably won't see the light of day for awhile. TCLN is supporting very bright people, IMO, and the ideas now available from genetic modifications of the tumor microenvironment are moving very fast in the drug-discovery business; both academically and within biotech industry.

Cancer Res 1996 Nov 1;56(21):4998-5004
A chimeric Lym-1/interleukin 2 fusion protein for increasing tumor vascular permeability and enhancing antibody uptake.
Hu P, Hornick JL, Glasky MS, Yun A, Milkie MN, Khawli LA, Anderson PM, Epstein AL
Department of Pathology, University of Southern California School of Medicine, Los Angeles 90033, USA.
A murine antihuman B-cell monoclonal antibody, Lym-1, has shown considerable promise for the treatment of human malignant lymphomas. To enhance its clinical potential, a genetically engineered fusion protein consisting of a chimeric Lym-1 (chLym-1) and interleukin 2 (IL-2) was tested for mediating cytotoxicity, increasing vasopermeability, and enhancing antibody uptake in human malignant lymphomas. The chLym-1/IL-2 fusion protein, which was expressed initially in a baculovirus system and more recently in the glutamine synthetase gene amplification system, was shown to be processed and assembled into a normal immunoglobulin monomer with two IL-2 molecules per antibody. It was found to be equivalent to the chLym-1 antibody in antigen-binding specificity and relative affinity. In addition, it maintains IL-2 cytokine activity as demonstrated by support of T-cell proliferation. Moreover, in antibody-dependent cellular cytotoxicity assays against Raji target cells, chLym-1/IL-2 had approximately 2-fold and 4-fold higher cytotoxicity than chLym-1 and murine Lym-1, respectively. Used as a pretreatment, chLym-1/IL-2 enhances the uptake of chLym-1 at the tumor site by altering the permeability of tumor vessels producing tumor:normal organ ratios of 420:1 for blood and 1708:1 for muscle at 3 days. The in vitro and in vivo activities of chLym-1/IL-2, therefore, suggest that this genetically engineered antibody fusion protein may represent a new immunotherapeutic reagent for the treatment of human malignant lymphomas.

 

Q. Regarding the chLym-1/IL2 fusion protein that you refer to in the 1996 paper...do you think that this sort of approach will someday make it to clinical trials and possibly eventually improve upon the current Oncolym? If so, roughly how close to clinical trials might it be?

Regarding fusion peptides in general, does anyone hold patents? are many scientists working on this approach? and how would the patents work? would separate patents be issued for specific peptide combinations, or is the entire "fusion of proteins" idea patentable?

Similarly, re the latest Epstein paper on chTNT-3/IL-2,if it is eventually determined that this approach improves upon current TNT (already in trials), do you still have to start trials from the beginning, or can you make modifications to a trial already in progress?

 

A. Your questions are thoughtful and insightful, unfortunately for me, they are also difficult to answer. Giving opinions during seminars or classes or at lunchroom discussions (which can be heated) is not quite as intimidating as talking out loud on an internet chat board. Hence, I believe I need to qualify my remarks as much as possible.

Regarding your first question about possible use of chLym/IL-2 fusion peptides. Certainly I believe the approach will be used in the clinic; whether it will be that particular combination of targeting/attached cytokine is entirely unknown. One parameter involves the therapeutic use of Lym-1 which is iodinated with a radioactive isotope and that is its source of cellular toxicity (the emission from the isotope). The chLym/IL-2 was used to target regions of tumor with subsequent changes in permeability of the vascular bed and is a different form of trying to enhance the therapeutic efficacy of other agents, perhaps drugs or delivery of antibodies.
Short answer, no, I do not believe that particular combination is close to clinical trials, especially with the ongoing studies in progress. But I do stress the idea bank is there.


Patents on fusion-peptides. Wow, what a lawyers delight! That’s my qualification on this one...I would have no idea of the patent messes one could get into, but I’ll bet they ain’t pretty. I will say that with regards to fusion-peptides that target vascular cells by means of a constructed antibody attached to some neat protein that would alter the properties of the endothelium in that region...that is covered (IMO) by Thorpe’s patent. Put a little more scientifically...the construction of fusion-peptides by means of the utilization of immunoglobulin genes with specificity toward endothelial antigens (no matter there presence, induction or ultimate expression) would be covered under the Thorpe patent. Other combinations of protein constructs would not be covered, IMO.

Finally, your last question regarding chTNT/IL-2 seems as complex as the first one. Tell you why. An analogy is the approved agent, Rituxan from IDEC. Since it is FDA-approved, it can be prescribed under conditions or combinations that may not have been ideal or optimal for its original intended use. IL-2 (free-form, as a protein in solution) is approved. It can be used in a variety of ways. Hence, their combination in different clinical settings is easy to do. But it is not easy to combine agents where one remains an experimental reagent. Regulations may require going back and looking at parameters that you don’t believe are necessary, but may have to do. Radiolabeled chTNT is a therapy molecule, but chTNT/IL-2 is a permeation enhancer using the target of TNT as a local place to dock the molecule. I realize my answers are not very enlightening, but escalating clinical trials and using combinations that make perfect sense can always be bogged down by layers of committees that exist all the way from the hospital to Washington.

 

02/07/1999

Previous post demonstrated earlier paper on the construction of a Lym-1/IL-2 fusion peptide; the targeting antibody sequence against NHL cells. The paper cited below involves the Lym-2 antibody, produced against chronic lymphocytic leukemia cells, and two cytokines; GM-CSF, a product of bone marrow macrophages and other cell types which aids in the maturation of immune cells and causes infiltration of cells into lesions (and by the way, activates macrophages to produce an enzyme which cleaves a serum protein to yield the famous angiostatin. A good cytokine. Also studied is the fusion of Lym-2/Il-2.

Blood 1997 Jun 15;89(12):4437-47

Chimeric CLL-1 antibody fusion proteins containing granulocyte-macrophage colony-stimulating factor or interleukin-2 with specificity for B-cell malignancies exhibit enhanced effector functions while retaining tumor targeting properties.
Hornick JL, Khawli LA, Hu P, Lynch M, Anderson PM, Epstein AL
Department of Pathology, University of Southern California School of Medicine, Los Angeles 90033, USA.
Although monoclonal antibody (MoAb) therapy of the human malignant lymphomas has shown success in clinical trials, its full potential for the treatment of hematologic malignancies has yet to be realized. To expand the clinical potential of a promising human-mouse chimeric antihuman B-cell MoAb (chCLL-1) constructed using the variable domains cloned from the murine Lym-2 (muLym-2) hybridoma, fusion proteins containing granulocyte-macrophage colony-stimulating factor (GM-CSF) (chCLL-1/GM-CSF) or interleukin (IL)-2 (chCLL-1/IL-2) were generated and evaluated for in vitro cytotoxicity and in vivo tumor targeting. The glutamine synthetase gene amplification system was employed for high level expression of the recombinant fusion proteins. Antigenic specificity was confirmed by a competition radioimmunoassay against ARH-77 human myeloma cells. The activity of chCLL-1/GM-CSF was established by a colony formation assay, and the bioactivity of chCLL-1/IL-2 was confirmed by supporting the growth of an IL-2-dependent T-cell line. Antibody-dependent cellular cytotoxicity against ARH-77 target cells demonstrated that both fusion proteins mediate enhanced tumor cell lysis by human mononuclear cells. Finally, biodistribution and imaging studies in nude mice bearing ARH-77 xenografts indicated that the fusion proteins specifically target the tumors. These in vitro and in vivo data suggest that chCLL-1/GM-CSF and chCLL-1/IL-2 have potential as immunotherapeutic reagents for the treatment of B-cell malignancies.

 

01/27/2000

Cancer Res 1998 May 1;58(9):1952-9
Vascular endothelial growth factor as a marker of tumor endothelium.
Brekken RA, Huang X, King SW, Thorpe PE
Cell Regulation Program, Department of Pharmacology, University of Texas Southwestern Medical Center, Dallas 75235-9041, USA.
Vascular endothelial growth factor (VEGF) is an angiogenic growth factor that is a primary stimulant of the vascularization of solid tumors. VEGF production is induced by oncogenic gene mutations in the tumor cells and by hypoxic conditions inside the tumor mass. Hypoxia and the locally increased concentration of VEGF lead to an up-regulation of VEGF receptor expression on tumor endothelial cells. Therefore, in the tumor microenvironment, there is an up-regulation of both VEGF and its receptor, leading to a high concentration of occupied receptor on tumor vascular endothelium. The VEGF:receptor complex presents an attractive target for the specific delivery of drugs or other effectors to tumor endothelium. In the present study, several hybridomas that secrete monoclonal antibodies against the VEGF:receptor (Flk-1) complex or against VEGF itself have been raised. Three of the antibodies (3E7, GV39M, and 11B5) bind with high affinity to the VEGF:Flk-1 complex in ELISA and to tumor endothelium in frozen sections of human tumors, rodent tumors, and human tumor xenografts. 3E7 and GV39M localize selectively to tumor endothelium after i.v. injection into mice bearing human tumor xenografts. Additionally, one antibody (2C3) was raised that blocks the interaction between VEGF and KDR/Flk-1. 2C3 inhibits VEGF-mediated growth of endothelial cells in vitro and localizes strongly to connective tissue in tumors after injection into mice bearing human tumor xenografts. These findings suggest that 3E7, GV39M, and 2C3 are candidates for targeting and imaging the vasculature or connective tissue of tumors.

 

Interesting twist the anti-VEGF thrust is taking...from many angles and corporate headings. IMCL has the IMC-1C11, an antibody targeted against the KDR receptor (I still believe the use of this antibody is in direct conflict with the Thorpe VTA patent), SUGN has the SU5416 which blocks the activation of the KDR receptor and now, the new Thorpe derived antibody, 2C3 which blocks the binding of VEGF to its receptor on tumor endothelium. These strategies, combined with the recent SUPG intent to license from Techniclone a VEGF-ligand construct to target tumor endothelium demonstrates the importance of this particular growth factor in the growth of abnormal, inflammatory-type blood vessel cells.

A question which has yet to be addressed in the science of tumor vasculature, as well as abnormal behavior of endothelial cells in other areas, such as macular degeneration and coronary artery inflammation that often follows angioplasty, as well as plaque formation is exactly how the membrane properties of these cells, expressing their newly formed VEGF receptors is different than normal cells that line blood vessels. Exploiting these differences is the grist for the mill of therapeutic approaches that are innovative with respect to molecular targeting of today's modern view of anticancer therapy. Certainly other target antigens, such as the expression of lipid molecules (addressed by Thorpe in recent studies) will come into play.

Knowledgeable people have told me that the VTA patent may cover distinct properties of "newly" formed vessels, compared to "old" vessels found inside the tumor, but I have not seen this addressed in the patent applications or issued patents. Other knowledgeable people have said that "just about anything that can be targeted to tumor endothelial cells is covered by the Thorpe studies".

How this can be partitioned out in licenses remains to be seen. Some may try to get it all, and at an unreasonable price or conditions with the company. ES and colleagues may hold their cards close to the vest as the financial conditions improve. Perhaps we can enter an era where we are have chips on the table in plain view, and the other players can not just bet pot-limit and take us out of the hand. We've been there, done that...but no more.

 

01/28/2000

Q. The use of TNT as an imaging tool has been discussed many times. This latest addition to our patent coverage brings up my question.
When used as a imaging technology, I'm assuming that lab trials will be done and biopsies performed after imaging to determine the precision of the read out. This process should be quite short as the biopsy can be performed immediately after the imaging. Hundreds of images and biopsies can be taken over a period of days/weeks. If successful, would the technique still have to be performed on humans to obtain FDA approval? Also, would this fall under IND or Medical Device in seeking approval? The use as an imaging tool seems to me to be something that could be brought to market in a very short period of time.

 

A. Well...just my opinion, since I have no experience in this end of the science. I would think that imaging doses of labeled TNT would be far less than any therapeutic dose, and would fall into the categories of agents such as contrast dyes, radionuclides like Tc which is used to light up bone metastasis, and Prostascint, things like that. Hence, I would look for quick studies on efficacy of this kind of application with a rather quick FDA process.

Of course, this topic brings up another quirk that gripes me...see, Terry, this is another topic that could be discussed publicly, in an exciting fashion by the company in a news release...

Something like..."New Applications for Vascular Targeting Discussed..."..etc. We just never seem to do so. Chew (remember him???) ought to be thinking about these corporate-minded issues...(duh, HELLLLLOOOOOOOOOO ASCO??????????).

regards.

 

01/28/2000

Very recent patents awarded to Thorpe. Certainly relevant to the patent estate of TCLN. Appear to be very specific claims regarding targeting to endothelial cell antigens.

Issued October 12, 1999. 5,965,132: Methods and compositions for targeting the vasculature of solid tumors. Describes the delivery of diagnostic or therapeutic agents via antibodies specific for the antigen formed by the conjugate of a growth factor AND its receptor (as opposed to targeting either one alone), including the induction of target antigens on endothelium.

Issued Dec 21, 1999. 6,004,554: Methods for targeting the vasculature of solid tumors. A clever notion of selectively suppressing certain antigens found on normal endothelium but inducing these antigens on endothelial cells within the tumor bed. Then antibody mediated targeting and delivery of diagnostics and therapeutics to the induced target antigen.

Issued Dec 21, 1999. 6,004,555. Methods for the specific coagulation of vasculature. Method of delivery clotting inducing ligands to the microenvironment of the tumor vasculature by a bispecific antibody construct that binds both a cell antigen and localizes the coagulation factor resulting in a clotting cascade that infarcts the tumor bed.

At the time of issue, these three patents were assigned to UT Texas. Certainly a broad-base repertoire of once again, innovative vascular targeting.

 

03/06/2000

Phil Thorpe gave a talk at the very prestigious Keystone conference this weekend in Salt Lake City. "Targeting Coagulants to Tumor Vasculature"..."We have induced major tumor regressions in mice bearing large solid tumors with immunoconjugates that destroy or occlude the vasculature of solid tumors. The immunoconjugates employ antibodies that recognize molecules that are selectively expressed on vascular endothelium in solid tumors. The molecules either occur naturally, (e.g., VCAM-1 or E-selectin) or can be induced on tumor endothelium (e.g., MHC Class II). The antibodies are linked to the extracelluar domain of the human coagulation initiating protein, tissue factor. Truncated tissue factor is a soluble protein that is virtually devoid of coagulant activity while free in the blood ciruclation, but becomes a powerful and specific thrombogen after binding to the tumor endotheial cell surface. Induction of coagulation by the targeted tissue factor requires exposure of phosphatidylserine (PS) on the endotheial cell surface. PS exposure is itself confined to tumor endothelial cells in mice. The need for coincident expression of the target marker and PS further restricts the action of the targeted tissue factor to tumor vessels. These new drugs have the potential for widespread application in the treatment of solid tumors.

 

03/31/2001

The annual meeting of the AACR focuses upon progress of older studies that continue down their natural evolution of knowledge and occasional wildcards of new, exciting fronts of basic science that lends itself rapidly to therapy (translational research). The overview I offer here is a result of my own interest and expertise and other researchers may have differing and argumentative views. I will start with very general notions of tumor biology and end with specific thoughts as to the science of cancer therapy.

The problems of identifying unique characteristics of cancer cells that can be subsequently exploited for therapy remain somewhat unchanged. A brief review is probably relevant, in order to assess where current research is headed. The heterogeneity of tumor cell populations is well established and, for the most part, the therapy of cancer is the therapy of metastatic disease. What makes therapy so particularly difficult it two-fold, (a) the more we uncover with regard to the genes and their products of both normal and cancerous cells the more we have to unravel intellectually about the constant interplay between metabolic pathways of cells that ultimately determine sensitive set-points of survival or cell death; and (b) the inherent genetic instability of tumor cells results in permutations, amplifications and redundancies that are difficult to attack.

It seems clear that tumor cells are able to subvert homeostasis, capture the advantageous elements within the tumor microenvironment and through their own evolution of selection for anonymous subpopulations of cells endowed with unique characteristics, cancer cells are showing us their ability to mutate and alter their environment in a manner that assures continued growth. Some investigators would argue that the focus should be entirely upon tumor blood vessels and their particular properties since the expanding tumor mass ultimately depends upon a viable blood supply, but I suspect this will be shown to be not sufficient. I imagine we will find that the properties of the tumor vasculature are constantly being modeled and shaped as a result of intimate communication that takes place between tumor cells and their blood supply.

 

Current thinking about direct therapy is aimed squarely at the tumor cells (as always) and the blood vessels of the tumor. Keep in mind there is a probably a great difference between trying to "prevent" metastatic growth of a tumor and the direct treatment of established metastases or primary tumor, even with regard to the properties of the endothelial cells. Most hard information at the present time is coming from studies of established disease, even in the animal models. Current efforts seem to center upon the knowledge about what tumor cells need to do in order to sustain signaling for continued growth, induce a blood supply and make it all work in a constantly changing tumor mass. The secretion of growth factors such as bFGF, VEGF, EGF, TGF-alpha, IL-8, IL-6 and the expression (and secretion) of a variety of metalloproteases (MMPs), together with the loss of certain adhesion molecules and the upregulation of a vareity of genes that promote drug-resistance, avoidance of programmed cell death events (such as the Bcl-2, bax family of genes), and activation of cell cycle pathways (p53 mutations, PTEN alterations, CDK genes) all make for a hungry, aggressive population of cells ready to take on the battles of host response and intervention. In addition, tumor cells upregulate and express a variety of growth factor receptors that can be auto-stimulated and the signaling from these receptors activate survival pathways for the cells. The question becomes, in the research, how to categorize and make sense of the vulnerabilities of the tumor, taking into account the needs of normal tissue limits to our assaults.

Progress in identification of unique molecular expressions of tumor cells and endothelial cells from solid tumors is being made with respect to the "chip array" technology. DNAchips, RNAchips, CD-expression arrays and proteomics (still mainly limited to mainstream 2-dimensional gel techniques) are showing a multitude (too many) of genes and proteins that are somewhat unique to the tumor with respect to normal tissue around the tumor, or of endothelial cells isolated from tumor. Unfortunately, the mass of information is not easily translated to bench experiments about whether the identified proteins are viable targets for therapy. Yet, the wealth of information (say in identifying that certain growth factors go up, certain receptors are present, certain molecules are being secreted) lends itself to putative targeting for therapy. With respect to direct therapy that results from the knowledge of reading the 10,000 genes off of a DNAchip, we ain't there yet. Most of the data are about genes we already are targeting. But the information is coming.

 

Modern therapy still is focused upon 4 main areas, (a) direct cytotoxic agents aimed at tumor cells, especially specific genetic defects of tumor cells, (b) direct inhibition of tumor blood supply, (c) immunotherapy and (d) gene therapy. I shall write little about gene therapy, due to the limitations of trying to insert "corrective" genes into a tumor mass (not convincing) and the clinical troubles resulting from Pennsylvania studies about a year ago, most gene therapy is at a halt. Let's work somewhat backwards…

Immunotherapy (my own field of experience) remains a mysterious realm of intrigue and heart-breaking experience that has persisted for three decades. Modern techniques of dendritic cell isolation and "loading" with tumor antigens is very promising, but seems limited at the moment to tumors that we knew were somewhat recognized by the immune system, such as melanoma and renal cell carcinoma. Good progress is being made about the requirements of antigen-presenting cells that result in a demonstrated immune response against tumor, but these studies are fraught with modulation due to the presence of an overwhelming amount of immune cytokines within tumors (interleukins 2, 4, 5, 6, 10, 13, IL-1, TGF-beta, TNF-alpha, GMCSF, for example) and various leukocyte populations that have defects and can be immunosuppressive; we still wait for some definitive insight and breakthrough experience in this area.

Tumor cell cytotoxics are taking two paths; (a) more and more toxic agents that just plain kill cells (such as the CPT-11, gemcitabine, etc) and (b) agents that target the growth factor requirements of tumor cells. We can not ignore (a) in the context of (b)…and I will explain.

It is well-established that targeting of growth factor receptors (such as the EGF-receptor, PDGF-receptor, VEGF-receptor) on both tumor cells and endothelium that make up the blood vessels of tumor cell masses (more on that later), is a fast-moving, aggressive field of current therapy. The obvious examples are the Herceptin antibody directed against EGF-r on breast tumor cells, C225 directed against the same...and in various stages of clinical trials and several antibodies against the VEGF-receptor. The other strategy is the use of small molecule tyrosine kinase inhibitors against the growth factor receptors, such as the marvelous STI571 against the mutated PDGF-r in chronic myelogeneous leukemia (it seems there are variant subpopulations emerging in some of the "cured" patients that have further mutated this kinase and is not targeted by STI571). These tyrosine kinase inhibitors seem to come out of the woodwork…besides the known SUGN compounds, now Novartis has a couple of very promising agents, (PKI166, PTK787) that inhibit the growth of tumor cells by blocking the activation of their growth factor receptors.
Now, here is where the twist on these agents become very interesting. There must be 25 new tyrosine kinase inhibitors indentified (we only need a few, excuse me) that target the common growth factor receptors of EGF, VEGF and PDGF. However, some new ones are against what is known as downstream signals (into the areas of what is called MAP kinases, NFkappaB, CDKinases) which are exciting new targets, but I suspect not much better than hitting the initial receptor. Let me say this another way…when the needed survival and growth factor, such as EGF (or its analog, TGF-alpha) binds to the receptor on tumor cells (or some endothelium) it promotes cell division, stabilization and survival. To target that receptor is excellent…but one can also go after those events that take place inside the cell after the EGF bound the receptor…in other words, the "downstream" events. These cascades are complex, redundant and yet new targets can be found, many involving kinases of a different variety. A lot of studies have identified these targets, and there were at least three full sessions devoted to new tyrosine kinase inhibitors.

 

Let's talk tumor vasculature, before we combine the cytotoxic agents and the growth factor receptor inhibitors, for common threads are now being observed. It is obvious to anyone who reads of modern tumor therapy that inhibition of angiogenesis (the formation of a blood supply) is the exciting feature of cancer research. Exciting because of the hope and promise of taking away the blood supply of tumor, resulting in a collapse of tumor growth and sustained dormancy of remaining tumor cells…and perhaps the inability of tumors to induce the needed blood vessels for growth of other tumor deposits not actually detected (occult metastatic disease).

When one considers the physiology of the formation of a new blood supply, one finds that this event (say, in normal wound healing or menstruation, or embryogenesis), the migration or differentiation of endothelial cells that form the new vessels undergo an extemely complex set of moves comprised of cell division, migration, tubular formation, establishment of cell-cell contacts and eventual stabilization into blood vessels that have functional viability. It seems clear that tumor blood vessels differ with respect to other tissue blood vessels with regards to the expression of cell-surface molecules, such as integrins, collagen products, matrix proteins, growth factor receptors, angiopoietins, lipids and a variety of different genes (identified through the chip arrays mentioned before). This makes them "targetable" and forms the basis of studies and clinical trials using inhibitors of angiogenesis, such as interferon-alpha, angiostatin, endostatin, 2ME2, combretastatin, thalidomide, specific integrin antagonists, antibodies directed against markers on endothelial cells and perhaps even low-dose chemotherapy. Make no mistake about it…this is THE area of aggressive preclinical and clinical studies, the potential of targeting the blood supply of tumors. Pasqualini and her colleagues have published exciting work in the area of phage-identification of endothelial cell targets, which are a whole new set of potential proteins found on exclusively on tumor endothelium that may serve as viable targets for shutting down the blood supply of tumors.

 

However, the situation becomes more complex (sort of a "but wait, there's more"). It turns out that many of the same growth factor targets found on tumor cells are also found on tumor endothelium. The implication of this is as follows…suppose a tumor requires the expression of the EGF-receptor for optimal growth and one observes that an antibody or tyrosine kinase inhibitor of that receptor inhibits directly the tumor growth. Well, in addition, it has been observed that the tumor endothelial cells are likely to upregulate their receptors for EGF also, and the inhibitor becomes a TWO-pronged attack, both tumor and vasculature. Moreover, preclinical studies at AACR showed that if one treated tumors (in animals) with BOTH cytotoxic agents (such as CPT-11, taxol or gemcitabine) PLUS the growth factor inhibitors, one obtains superb inhibition of tumor growth (and metastasis) compared to the use of either agent alone. This is not a trivial observation. It suggests that the optimal attack on tumor, at the moment, remains the use of cytotoxics combined with antiangiogenic agents. I doubt that single agent use of pure antiangiogenic compounds will achieve near the effect as combination therapy with standard cytoreductive therapy.

An additional note on tumor vasculature leads us to the PPHM VTA targeting…that is, the propensity of tumor beds to have a "coagulytic" environment. Essentially this means that the vessels found within tumor masses have properties conducive to coagulation, a process found normally only in the immediate environment of a wound or repair process. They are "setting on the edge" with exposed molecular structures that are optimal for one juicy blood clot if saturated with the right agents, such as Tissue Factor. This is a unique and unexplored area (except for Thorpe and a couple of groups) that is ripe for harvest. The transition to this subject will lead me to comments of the PPPH-related abstracts found this year at the AACR.

 

Abstract from Epstein group.

Recombinant Truncated Tissue Factor/Rgd Fusion Protein as a Target Anti-Vascular Therapeutic Agent
Peisheng Hu, Qing Zhou, Thomas Bai, John Shariff, JiaLi Li, Alan Epstein, University of Southern California, Los Angeles, CA.
Rapidly proliferating tumors require an efficient blood supply to meet their nutritional needs in both primary and metastatic diseases. Tumor vasculature is a particular suitable target for cancer therapy because it is composed of nonmalignant endothelial cells and those cells are genetically stable. In this study, truncated tissue factor fusion protein chTNT-3/tTF, chTV-1 and RGD/tTF have been constructed. Truncated tissue factor (tTF) is a 25 KD soluble protein whose membrane binding domain has been deleted. It has the factor VII activating capacity of its parent protein. Monoclonal antibodies chTNT-3 and chTV-1create a binding domain which targets the thrombogenic capacity of the tTF to the tumor vasculature, therefore initiating coagulation and occlusion of blood flow within the tumor. The glutamine synthase gene amplification system was used for statement of these two fusion proteins. A motif contains sequence Arg-Gly-Asp (RGD) has been identified integrin primarily expressed in tumor vasculature, RGD/tTF has been inserted into pQE60 and expressed in Top 10. The statement of chTNT-3/tTF and chTV-1/tTF has been done by standard ELISA assay, and Coomassie Plus Protein Assay Reagent Kit has been used for RGD/tTF. Animal studies showed that RGD/tTF had been completely removed 12 hours after injection, biodistribution study demonstrated that tumor has higher uptake of fusion protein compared with other organs, and tumor had obviously necrosis due to the treatment. These results showed that tTF linked to monoclonal antibody and RGD may be effective immunotherapeutic reagent for the therapy of cancer.
Comment: [This study demonstrates that not only can the truncated tissue factor protein be targeted to the endothelial cells within a tumor, and results in a choking of the tumor blood suppy in the tumor microenvironment, but that this molecule can be hooked to the TNT family of antibodies which are highly specific for the tumor cells and give rise to the same phenomenon. This finding expands the concept of targeting the tumor vasculature to include effects from also targeting antigens found within the tumor cells. Hence, the ARCUS venture of VTA can include the TNT antibody as well as Thorpe lab-derived targeting molecules. Advantages include the rapid clearance of this targeting antibody and tTF construct from normal tissue, and the specific localization within tumor compared to normal tissue.]

 

In Vitro and in Vivo Studies of VEGF/RGEL Fusion Toxin Targeting Tumor Vascular Endothelium.

Hangqing Jin, Sophia Ran, Philip Thorpe, Michael G. Rosenblum, The University of Texas, MD Anderson Cancer Center, Houston, TX; UT Southwestern, Dallas, TX.
Vascular endothelial growth factor (VEGF) is an angiogenic growth factor which binds to two
structurally related tyrosine kinase receptors denoted KDR/FLK-1 and FLt-1. Both KDR/FLK-1 and Flt-1 are overexpressed on the endothelium of solid tumor vasculature. Therefore, the receptors for VEGF appear to be unique targets for the development of therapeutic agents that may interfere with tumor growth and metastatic spread through inhibition of tumor neovascularization. We created a fusion construct of VEGF121 and the plant toxin gelonin (rGel) and the resulting VEGF121/rGel fusion protein demonstrated the biological activities of both VEGF and rGel components. Porcine Aortic Endothelial cells were transfected with either flt-1 (PAE-flt) or KDR/flk-1 (PAE-KDR) and utilized to examine whether KDR/FLK-1 or Flt-1 play a role in cytotoxicity of VEGF121/rGel. Log-phase PAE-KDR cells were ~900 fold more sensitive to VEGF121/rGel compared to rGel (I.C.50 of 0.5 nM vs 450 nM respectively). The PAE-flt cells demonstrated no selective sensitivity to either the fusion toxin or free rGel (I.C.50450 nM). Western analysis demonstrated increased auto-phosphorylation of the KDR receptor after exposure to either VEGF or VEGF121/rGel. Dose-response and time courses for this effect were identical for both agents. As expected, neither VEGF nor VEGF121/rGel were able to induce autophosphorylation of flt-1 expressing cells. These data suggest that the KDR receptor is primarily responsible for development of VEGF121/rGel cytotoxicity. Studies to examine the binding, internalization and intracellular routing of VEGF and VEGF121/rGel after binding to the two receptors are ongoing. In nude mice bearing PC-3 prostate tumors, IV treatment (q 48h X 5) with total doses up to 20 mg/kg results in impressive suppression of tumor growth compared to controls. Pharmacokinetic studies of the VEGF121/rGel fusion construct will also be reported. These data suggest that this construct has significant potential for clinical use in reduction or prevention of metastatic spread.

Comment: [This is a "trojan" horse approach to vascular targeting, in that the statement of this particular VEGF-receptor on tumor endothelial cells, in contrast to "normal endothelium" makes the attachment of the toxic compound (the gelonin) target only these type of cells in a specific manner. Since the VEGF-construct will "seek out" the receptor on the tumor endothelium, it will deliver this toxic payload to these cells and destroy their ability to support a blood supply to the tumor. Animal data presented that was not included in this abstract was a >85% reduction in growth of the A375 human melanoma in nude mice, as well as >90% reduction in growth of the PC-3 prostate cancer in nude mice. In fact, the prostate cancer seemed to be a flat line of a very small tumor nodule as a function of time throughout the study, with exponential growth of the control-treated tumor. This particular therapy appears to be what SUPG has in mind concerning their interest in the PPHM collaboration (see press release of 13 Feb 2001 regarding targeting the VEGF receptor)]

 

Expression of VCAM-1, E Selectin and PSMA on Human Normal, Malignant and Inflamed Vessels.
Sophia Ran, Maria Sambade, Philip E. Thorpe,
Southwestern Medical Center, Univ. Dallas at Texas,Dallas, TX; Southwestern Medical Center, Dallas, TX.
An ideal marker for targeting tumor vasculature would be a luminal protein that is expressed on a high proportion of tumor endothelium and absent from normal vessels. Success of the targeting approach will ultimately depend on the extent of a marker's statement, its consistency and favorable distribution of positive vessels within the tumor vasculature. It should be also considered whether a marker is present at sites of inflammation, tissue re-modeling and other pathological non-malignant conditions that might be found in cancer patients. We examined immunohistochemically the statement of three vascular markers of human solid tumors: vascular cell adhesion molecule-1 (VCAM-1), E-selectin and prostate specific membrane antigen (PSMA). It has been previously shown that these markers are upregulated on the tumor vessels in various malignancies but the comparative analysis of the pattern of their statement has not been done. The staining of normal, malignant and inflamed human tissues with anti-VCAM-1, E-selectin and PSMA antibodies was analyzed according to the following criteria: a) the percentage of positive vessels compared to total, CD31-stained vessels; b) the intensity of staining; c) the pattern of distribution of positive vessels (focal, central, peripheral, patchy or random). The overall vascular statement in malignancies was compared to that in normal and inflamed tissues. PSMA was the most abundant and consistent marker, being present in all 12 different types of tumors studied. The percent of PSMA-positive vessels ranged from 10% in lymphomas to 80% in renal and breast carcinomas. Normal vessels were devoid of PSMA with the exception of endometrium, ovary and adrenals. PSMA was also strongly upregulated at inflammatory sites, such as colitis, cystitis and reactive tonsil. VCAM-1 and E-selectin were found in 9 and 7 out of 12 tumor types, respectively. The proportion of positive vessels (5 to 50%) was smaller than for PSMA. VCAM-1 was present on 5-10% of normal vessels in kidney, thyroid and endometrium, whereas E selectin was completely absent from normal organs. VCAM-1 also prevailed in the inflammatory sites while E-selectin did not. This analysis suggests that: a) all three markers are upregulated by inflammatory or angiogenic conditions; b) PSMA is an attractive marker because of its widespread and consistent statement in various tumors; c) E-selectin is an attractive marker because it is the most selective tumor endothelial cell marker, and is moderately to strongly expressed in Hodgkin's lymphoma, non-small cell lung carcinoma
and breast tumors.

Comment:[This study falls right into the lap of the Thorpe patent estate on molecules uniquely targeted on tumor vasculature. This study is important for in HUMAN tumors, they determined whether or not these molecules they want to target, (E-selectin, VCAM-1 or PSMA) are widespread in inflammatory conditions (which patients may have besides their growing tumor) and on normal tissue. The attractiveness of the two molecules (PSMA and E-selectin) verifies the approach Thorpe has taken for the VTA. Now, whether PSMA falls under the Cytogen claims or not is a consideration for the company (?????) but the science is solid. Note the number of tumor types (lymphoma, lung, breast) that carry these markers, making it of broad applicability, as desired. This type of targeting can be hooked to a variety of toxic compounds, or using the tTF (truncated tissue factor)].

 

Angiogenesis as a Determinant of Tamoxifen Response in a MCF-7 Breast Cancer Xenograft Model of Resistance
Rachel Schiff, C Kent Osborne, Philip E. Thorpe, Sophia Ran, Rolf A. Brekken, Irma Parra, Syed K. Mohsin, Suzanne A. Fuqua, Baylor College of Medicine, Houston, TX; The University of Texas at Dallas, Dallas, TX; The Hope Heart Institute, Seattle, WA.

Angiogenesis is known to be important for the prognosis of breast cancer -- cancers with high microvessel counts are associated with increased recurrence and poorer outcome. Less is known, however, about angiogenesis as a predictive marker in breast cancer. Pilot clinical studies suggest that high vessel counts are associated with a reduced response to the antiestrogen tamoxifen. We therefore utilized a xenograft tamoxifen-resistance (TR) model to examine gene statement profiles associated with the development of the resistant phenotype. Using Clontech cDNA arrays, we found that several angiogenic factors and receptors for these factors were changed in statement as resistance developed. Among these, total VEGF was reduced in the TR tumors, while a specific potent isoform, VEGF121, increased. Flt-1, a VEGF receptor, was also found to be upregulated in the TR tumors. Thus, we hypothesize that VEGF121 and its receptor may be important determinants of resistance. To test this hypothesis we are targeting the VEGF receptor complex to reverse or delay the development of resistance in the xenograft model. Interestingly, when microvessel density was determined using an antibody to CD31, we did not see a major increase during the development of resistance. This suggests that these angiogenesis-related markers may have roles beyond direct stimulation of microvessel density in the development of tamoxifen resistance in breast cancer.

Comment: [The purpose of this study was to target the VEGF-receptor within human breast cancer growing in nude mice. This study confirms the possibility that VEGF itself is a "survival" factor for new blood vessels within a tumor (some studies have shown that anti-blood vessel effects from some compounds can be abrogated by the presence of EGF or VEGF). Can we actually take advantage of the presence of this survival factor? Modern technique of the DNA array shows that molecular analysis of the tumor can lead to choosing important molecular targets…nice modern approach]

 

06/05/2001

There are opportunities for the company to demonstrate scientific excellence and progress in the preclinical and clinical evaluation of their approaches to the therapy of cancer. There are periods of time where there is nothing much that can be said (for instance, during the treatment and follow-up phase of a clinical trial where one is waiting on parameters of response that can be measured) and sometimes there are rapid opportunities such as society meetings, conferences, licensing deals and significant management decisions that can be made available to the shareholders. In my opinion, any legitimate opportunity to update the progress of the technology in the area of research and clinical trials must be seized and handled with professional savvy.

First, there must be an commitment by management to constantly demonstrate visibility in the medical center, be it at the lab bench with preclinical studies or at the bedside with trials of the new products under clinical evaluation. In my opinion, there are no good strategies that involve silence about the science or the clinic. Second, there is no place to hide in the medical center. If a new therapeutic agent or procedure is good, really good, people will know. Of course, one must have superb experimental design for the studies, execution of the trials by knowledgeable and excellent physicians and wisdom and proper insight about clinical parameters
 

With these introductory remarks, I find it unacceptable that the company would not follow up their press releases announcing presentations of preclinical studies at AACR and the Thorpe presentation in Seattle. Moreover, I was encouraged by the ASCO data on glioma, but left pondering exactly how the neuro-oncologists view the use of Cotara in therapy of brain cancer. Let me explain this latter comment in detail.

Regarding the ASCO results from the Phase II brain cancer study: Newly diagnosed or recurrent brain tumors have to be one of the most complex clinical issues in oncology to evaluate. When one considers Phase I and Phase II studies in glioblastoma (or anaplastic astrocytoma) the patient population can quickly be obscure. The single clinical parameter discussed in the news release (which is all we have available for interpretation, other than the abstract) was median time to progression which was about 75% longer for treated patients compared to "historical controls". Patel was quoted as being "enthusiastic" regarding the potential of Cotara in treatment of both newly diagnosed and recurrent malignant gliomas, even compared to "standard therapy". What was NOT presented was an analysis that allowed definitive conclusions and comparisons to be drawn in light of many other Phase I/II studies in glioma. For instance, should one examine the responses of patients with recurrent disease (many prior therapies?) in light of only that specific patient population? I assume they did. What about the few newly diagnosed patients? How did they do (no real mention of two types of patient groups) compared to newly diagnosed patients that undergo other "standard" therapies? What were the differences between patients that received only one dose of Cotara versus two? What about the subsequent quality of life, regarding neurological defects of brain cancer therapy, behavior and well being? Is there a subset of glioma patients that benefit more from Cotara that other patients, perhaps by virtue of their prior therapies, or initial size of tumor, or features of the histological invasion of surrounding normal brain? ? The competition at medical centers is usually pretty active among clinical trials. Is this a treatment where Patel is enthusiastic enough to attempt to "recruit" patients to Cotara?


There may be limitations to the use of Cotara in brain cancer. The design of the Phase III trials may be restricted to patient populations that are well defined in clinical parameters that we know will be responsive to Cotara therapy in a fashion that offers a new viable option for their treatment. The results may be encouraging enough to attempt other forms of brain metastases such as those that occur from primary breast or lung cancer. Without publication of these data and hard analysis that is expected in the clinical community, that portion of the potential of this form of therapy in brain cancer remains elusive to the public.

 

Now…why press releases announcing presentations at AACR without any follow up? Perhaps they were about preclinical (animal) studies that did not constitute "blockbuster" news. So what? It was an opportunity to write about the progress of the science in the lab. I found the presentations significant. I assume portions of these studies are supported by the company; hence, they should have been presented to the shareholder. For example, Thorpe's paper entitled "Recombinant Truncated Tissue Factor/Rgd Fusion Protein as a Target Anti-Vascular Therapeutic Agent" involves cutting-edge research on targeting the blood supply of tumors and should be in clinical trials as soon as possible. This paper represented an opportunity to talk about the PPHM/OXGN venture (Arcus), the timelines for potential trials, the importance of this work and how it represents the modern thinking of two-compartment targeting of cancer (the tumor cells and their blood supply). The Thorpe and Rosenblum paper entitled, "In Vitro and In Vivo Studies of VEGF-RGEL Fusion Toxin Targeting Tumor Vascular Endothelium" was an excellent opportunity to update the findings of excellent reduction in tumor growth in the animal studies and speak to the SUPG/PPHM alliance regarding the use of VEGF targeting. Another opportunity missed. The Thorpe paper entitled, "Expression of VCAM-1, E Selectin and PSMA on Human Normal, Malignant and Inflamed Vessels" was an excellent chance to speak about newly identified vascular targets that may be exploited by the scientists of PPHM and represent future directions for clinical studies of targeting blood vessels of tumor. These studies demonstrated forward thinking and expansion of earlier work by Thorpe. Finally, the presentation by Rachel Schiff (Thorpe as co-author), "Angiogenesis as a Determinant of Tamoxifen Response in a MCF-7 Breast Cancer Xenograft Model of Resistance" spoke of potential targeting of the VEGF-receptor on blood vessels, a potent and modern approach to combination therapies of several different cancers in the clinic today. Unfortunately, we chose to remain silent, not out of "strategy" but perhaps out of lack of an aggressive philosophy to make the science of PPHM visible.

Finally, there was the Seattle presentation by Thorpe (and Rosenblum) regarding a summation of the modern approaches to vascular targeting, once again discussing the specific targets mentioned above, such as VCAM-1, PSMA, VEGF receptors (and their complexes) and the lipid, phosphatidylserine, which we will hear more about someday. Another wonderful opportunity for a powerful follow up of a news release that got buried only within the schedules of the shareholders with little visibility to the biotech investor community that would be seeing the name of PPHM emerge out of the mass of new attempts at cancer therapy.

It is disappointing to see theses opportunities go by. Now, later this month, we have Cotara data out of Mexico City to be presented at the Society for Nuclear Medicine. Once again we had the news release about the presentation of this Phase I trial by Cesarman. I wonder what the follow up will be?

 

06/13/2001

AVN (via Xenerex) has interesting methodology of generating human monoclonal antibodies to self-antigens. I wonder what target(s) PPHM has in mind. Several recombinant DNA technologies exist (probably all under patents)for the creation of antibody-fragments that can bind to the antigens in question. I wonder if the VTAs will continue to be created as Thorpe described in this paper from January.

Biotechniques 2001, Jan; 30(1): 190-194
Generation and characterization of recombinant vascular targeting agents from hybridoma cell lines.

Gottstein C, Wels W, Ober B, Thorpe PE.

University of Texas Southwestern Medical Center, Dallas, TX, USA.

Vascular targeting agents (VTAs) can be produced by linking antibodies or antibody fragments directed against endothelial cell markers to effector moieties. So far, it has been necessary to produce the components of VTAs (antibody, antibody fragment, linker, and effector) separately and, subsequently, to conjugate them by biochemical reactions. We devised a cloning and expression system to allow rapid generation of recombinant VTAs from hybridoma cell lines. The VTAs consist of a single chain Fv antibody fragment as a targeting moiety and either truncated Pseudomonas exotoxin (resulting in immunotoxins) or truncated human tissue factor (resulting in coaguligands) as effectors. The system was applied to generate recombinant immunotoxins and coaguligands directed against endoglin, vascular endothelial growth factor (VEGF):VEGF receptor (VEGFR) complex and vascular cell adhesion molecule 1 (VCAM-1). The fusion proteins exhibited similar functional activity to analogous biochemical constructs. This is the first report to describe the generation and characterization of recombinant coaguligands.

 

The Xenerex subsidiary almost seems a "contract" facility to produce human monoclonal antibodies against target antigens of the client's choice. Using the PR as a guide, it appears we have chosen to enter a "collaborative" agreement with AVN regarding the development of these antibodies. I imagine, from a business point of view, it is a path that allows future payments against present success. That is…we want them to produce human monoclonal antibodies against our selected target antigens, which is an expensive process (and all methods are fraught with patent infringement problems; including construction of fusion peptides), so we enter a joint venture with them that may include milestones and rewards.

What are the target antigens? That's the neat question. Well, PPHM is a vascular targeting company. With the exception of Lym-1 antibody (Oncolym when radiolabeled with I-131) that targets leukemia cells and TNT which delivers intracellular radiation (or, in theory, drugs) to the cell interior, the VTAs of ARCUS and PPHM are seeking targets on the blood vessels of tumors. Many of these targets are self-antigens.

Example: Prostate Specific Membrane Antigen (PSMA) is found on tumor endothelium. Thorpe is very busy studying this protein as a target for vascular targeting. But, PSMA is a self-antigen, meaning that since it is a protein that we have circulating in our bodies all the time…we can NOT raise antibodies against it (except using mice). Well, we don't want mouse antibodies for a variety of reasons, so we need human antibodies to use to target the PSMA on the cells of the tumor blood vessels, but the Xenerex technology knows how to "break our tolerance" against this PSMA, and can produce human antibodies against it. We can then make tons of the stuff and have a targeting antibody. The same can be said for other antigens that Thorpe has identified on the surface of endothelial cells that may be "self-antigens". Hence, the AVN methods are very useful. It will be extremely interesting to see if a couple of self-antigens, such as the phosphatidylserine complexes described in his Cancer Research paper of last year can serve as targets. But Thorpe has also described methods in the Biotechniques paper that I mentioned earlier today. Only he and the big guns at PPHM know what avenue they are taking on these studies.

AVN? Yes, a collaborator…but remember, with PPHM in charge and control. Regards.

 

07/31/2001

Oakwood and PPHM

The simple view.

This joint venture with Oakwood Labs opens a new application of the TNT antibodies in targeting. Liposomes (microscopic, spherical globules usually constructed of synthetic lipids or fats) contain empty spaces that can be loaded with all kinds of drugs, reagents, genes, toxins, and immunomodulators to name a few. When injected intravenously, the liposomes are readily absorbed and taken up by phagocytes in the blood, trapped in the liver and taken out of the circulation in the lung and spleens. It is necessary to devise tricks in the composition and targeting of the liposomes to get the specificity of delivery to site of tumor cells.

Loading (attaching) antibodies specific for tumor cells and a variety of other means can increase this specificity. Oakwood is working on a therapy of colon cancer and need to have great specificity for the regions of tumor cells…since the liposomes will not last long in the liver tissue. They have chosen to partner with PPHM in targeting by using the TNT antibody, which is highly specific for tumor tissue. Of course, this approach is not limited to colon cancer mets in the liver…but is applicable to a wide range of solid tumors.

These preclinical studies should be extremely interesting for Oakwood and PPHM and the general applicability of this technology will have implications for a variety of compounds delivered in this manner.

This approach can be a very lucrative and productive form of targeted therapy.

 

08/31/2001

With respect to the license by PPHM of the antibody technology that targets the cell surface lipid, phosphatidylserine (PS), the interest in this particular target is as follows. The stimulation of new blood vessel formation (which is continual in a growing tumor mass) and even the inhibition of normal blood vessel formation (as when a wound has healed) involves elements of the clotting-cascade, a complex set of serum proteins that ultimately interact in various ways to form clots. Hence, the blood vessels within a growing tumor are sometimes "thrombogenic", that is, they are setting right on the edge of "wanting to clot". About three years ago, Thorpe demonstrated that the targeting of truncated Tissue Factor (tTF, one of those clotting proteins) to the tumor blood vessels caused intratumoral clots, necrosis and inhibition of tumor growth. Part of the excitement of this methodology is based upon the lack of clotting found in "normal" tissues that could prove to be a clinical problem, such as clots elsewhere in the body.

Now, why was this phenomenon of clotting limited to the tumor endothelium? The answer seems to lie in the observations that (a) clotting requires a negatively charged lipid surface to speed along the chemical reactions of these clotting factors, and (b) the common lipid available for this function is phosphatidylserine and (c) many tumor cells and damaged or inflammatory endothelium express PS on their outer cell membrane.

He stained the tumorsof the mice with an antibody specific for PS and found this lipid on the surface of tumor blood vessels, but not on the membranes of normal blood vessels (and some very small tumors). Therefore, the success of the tTF therapy may have relied upon the expression of PS. However, conceptually, this means that PS itself becomes a potential target molecule for directing specific intratumoral therapy, such as attaching tTF to the antiphosphatidylserine antibody. I assume there must be interesting preclinical data on this concept to spark the act of PPHM wanting to license this conceptual targeting moiety.

Whether this approach falls under the VTA of Arcus versus the sole pipeline of PPHM is a subject, I'm sure, of a much longer essay.

Will write about the 2C3 license at a later time.

 

09/01/2001

The 2C3 is the designation for an antibody which targets the receptor for Vascular Endothelial Growth Factor (VEGF) on tumor blood vessels. VEGF is a protein is released by tumor cells in abundance, especially in areas of low oxygen or acidic pH, which is turn stimulates "survival" factors inside of blood vessel cells. VEGF also causes dramatic changes in the ability of blood vessels to allow nutrients across their lumens; all of its actions seems to serve to bring oxygen and nutrients and stimulate new blood vessel formation. The twist of this seemingly important target is that VEGF is important for normal cell function with different cell populations in the body. However, the receptors for this protein can be fairly selective, and the 2C3 antibody targets the one (KDR/flt-1) found on blood vessel cells within the tumor.

This "vascular targeting" by 2C3, that is, the ability to prevent the actions of VEGF on the endothelial cells by binding of the antibody to the receptor, and thus blocking the VEGF has resulted in impressive preclinical studies published from the Thorpe lab.

The licensing of this antibody from the UT System in Dallas is somewhat confusing, since TCLN licensed this methodology in 18 months ago (see PR dated 27 Jan 2000) and J. Bonfiglio commented on it about a year ago on the lab studies (see PR dated 15 Sep 2000). The statement at that time, was "We are planning to develop it as a stand-alone anti-angiogenesis inhibitor and with our joint venture partner, OIGENE, we are examining its use as a Vascular Targeting Agent." This statement seems vague, at best, about how they are going to develop this therapy. I do not understand what this "new" licensing is about.

As a side note, therapies that have been directed against growth factor receptors, such as the VEGF-receptor (which include others, such as the PDGF receptor, the EGF-receptor [IMCL C225]) invariably are best when used in combination therapies, such as being combined with chemotherapy and irradiation. In fact, it appears that inhibition of angiogenesis is best served by a two-compartment attack upon the tumor, the tumor cells themselves and the tumor blood supply. Most preclinical data support this concept.

 

09/02/2001

Arcus and PPHM

VTA, antigangiogenesis, Arcus and PPHM: I have re-read some statements from the conference call and looked at the recent science.

Two statements from the conference call imply the
relationship of targeting the vasculature in terms of targeting established blood vessels within the tumor and targeting newly developing endothelial cells in attempts to prevent angiogenesis (the formation of new vessels).

Now, the use of truncated Tissue Factor (tTF) in tumor tissue, which causes thrombosis has relied upon conjugation of the factor to an antibody for targeting, such as antiVACM-1 (originally published by Thorpe) or like the Italian study using antiFibronectin to deliver the tTF to the tumor blood vessel cells. This is vascular targeting with CONJUGATED antibody is the property of Arcus. This conclusions follows LeGere's statement, " Well, everything to do with the truncated tissue factor is within Arcus. Any conjugated vascular targeting agent is within Arcus. So the only thing that is outside of Arcus is nonconjugated antibodies for vascular targeting. Our lead compound within Arcus is going to be an antibody that uses the truncated tissue factor as the coagulation effector. We will move that into the clinic as soon as we can."

Hence, the use of NONCONJUGATED tTF as an effective agent (which takes advantage of the expressed phosphatidylserine lipid on endothelial cells; found to also induce thrombosis in a later study by Thorpe) is the property of PPHM, inferred by his statement later in the conference call, "I believe the nonconjugated tTF would be under Peregrine. I have to see some more data on that before we would move that forward, but Dr. Thorpe has got some tremendous research going on over there, and there is a lot of stuff he's working on that we haven't even told you about that we find very exciting, so we look forward to getting a whole bunch more products out of Dr. Thorpe into the future, and we are very excited about working with the University of Texas, Southwestern."

Now, combine this with the statement above, that everything to do with UNCONJUGATED antibodies is outside of Arcus means that the 2C3 belongs to PPHM where probably the conjugation of the antiphosphatidylserine antibody to tTF belongs to Arcus.

Finally, an important statement, "Our lead compound, which would be our 2C3, which I know you have all heard of, is our anti-angiogenesis drug. We want to move that into clinical studies. I think the important thing to remember about these other approaches, they are going to be what we call nonconjugated antibody, or other people maybe call them naked antibodies. Big pharmas love naked antibodies. They are easy and cheap to manufacture. They can put a 30000 liter reactor on line and pump these things out day after day, and that's really what Rituxan and Herceptin, both of those drugs are naked antibodies, so the big pharmas love them, and those are the types of companies we will target with these programs.
The other one, we'll release more data on the other ones a little bit later. I don't want to kill a surprise that will be coming up later this year." This certainly suggests that either licensing or pharma partnership about the antiPS antibody or related methodology is in the works and will be a significant announcement.

 

09/09/2001

Zevalin and Oncolym:

Similarities: radiolabeled antibodies targeted against antigens found on lymphoma cells, primarily of B-cell origin. Both are murine monoclonal antibodies.

Differences: Zevalin is targeted against the external, cell-surface antigen, CD20, whereas Oncolym targets the external, cell-surface antigen, Lym-1, an altered HLA-Dr transplantation class antigen. Zevalin uses the yittrium-90 isotope, where the standard therapy with Oncolym is with I131 iodine (although DeNardo has used the 67-Cu isotope with a lym-1 antibody).

Zevalin is the IDEC attempt to answer the problem of probable rituxan resistance and their attempt to develop radiotherapy of lymphoma using the CD20 antigen. Oncolym remains a very viable candidate for therapy of B-cell lymphoma.

 

11/02/2001

Regarding ARCUS. One can only shake their head at the frustration that Thorpe must feel at the inability of his work to get into the clinic. The licensing deals, such as SUPG (the VEGF-directed targeting) are no doubt out of our control.

It may be more fruitful for Thorpe/PPHM to pursue the construct of humanized antibodies (via AVN, Xenerex) against the putative targets on endothelial cells of tumors that use unconjugated antibodies, which belong solely to PPHM and go from there.

 

11/02/2001

An example of the potential importance of intratumoral administration of Cotara is the China data on chTNT therapy of lung cancer. The patient population reported was a mixture of adeno, squamous, and small cell carcinomas. The partial and complete responses were noted in the group that received both intratumoral and intravenous administration of the chTNT, but we do not know if particular types of lung cancer were more responsive.

This issue of intratumoral administration should not be taken lightly, at least with the paltry amount of data in the public realm concerning Cotara. The data presented earlier this summer from Mexico by G. Cesarman was stated by the company, " The objectives of the study were to evaluate the efficacy, safety and dosimetry of Cotara for the treatment of primary and unresectable cancers of the pancreas, liver, prostate or brain. Depending upon the tumor type, Cotara was injected into the vein, directly into the tumor, into the spinal canal, or given in combination The drug was well tolerated. Positive responses were seen, including one prostate cancer patient with stable disease and one pancreatic patient with significant shrinkage of the tumor. The pharmacokinetics, biodistribution and dosimetry results showed that Cotara exhibited the expected patterns for a protein of its molecular weight and size. The dosimetry profile of Cotara showed that a good therapeutic dose was administered to the tumor", implying once again, any type of reduction of tumor was most likely in groups that received intratumoral administration of Cotara.

Whether this route is necessary (without large dose escalation in using intravenous administration) in the trials on biliary, pancreatic, soft tissue sarcoma and liver cancer at Stanford and Mayo is not known. Perhaps the nearest entry artery of some of these specific organs that contain tumor, such as pancreas or biliary duct or liver could be cannulated for direct infusion of Cotara, with a subsequent optimal therapeutic ratio of uptake of Cotara.

 

11/29/2001

Q. Have we seen or have we checked for any attachment of Cotara to malignant cells within the blood stream when injected intravenously?

 

A. The target antigen(s) of the TNT family of antibodies are DNA-associated proteins (mainly histones). These are intracellular antigens that are not normally exposed on the surface of cells, except for conditions of cell death, or necrosis. Tumors of any size ultimately develop areas of necrosis, which makes them targets for localizing the radiolabeled TNT antibody, such as TNT-1 or TNT-3. As cells die...say, during therapy (or even during irradiation therapy or chemotherapy), the number of target antigens gets larger for the TNT infusion.

Hence, viable tumor cells that float in the circulation are, in principle, not "seen" by the TNT antibody since they have no exposed histones. Yes, TNT would bind to floating dead, junky, crappy tumor cells, but they ain't gonna do anything anyway. Remember...the really excellent part of the original Epstein science on developing the TNT antibodies was the premise that, for the most part, immunotherapy with antibodies depends on the expression of the target antigen externally (on the cell membrane) by the cancer cells. This is why, ultimately, tumors develop resistance...such as the case of rituxan, bexxar, and even presumably oncolym. Because you select for the presence of the very, very small subpopulation of cells that do not express the target antigen. Epstein went a step further, and chose antigens that rarely mutate, and are always present...cause they are "normal" proteins that are only "recognized" when cells are necrotic.

 

12/13/2001

Brief view of today's news. The PR has been anticipated, since the FDA did grant a Fast Track review process for Cotara in glioma, and EL made a strong point of receiving a go-ahead by the end of the year.

There is only one source of hard data about the Phase II results with Cotara, and that is the ASCO meeting abstract of last May. Several items need to be noted: (a) the data presented at ASCO included 20 patients, 15 of which were either newly diagnosed or recurrent glioblastoma and 5 with recurrent anaplastic astrocytoma., (b) the stated results focused upon parameters of treatment, with a mention of median time to progression as one endpoint, being about 16 weeks (later revised to 13.5 weeks in the ASCO news release) for the group, compared to 8 weeks for historical median time of progression of about 8 weeks, and (c) the patient selection was not randomized, meaning a select group of patients was chosen for this Phase II study.

In the absence of a formal publication by Patel, et al., which describes in detail the patient populations treated and an analysis of both patient and treatment parameters that would allow definitive measures of antitumor response, the duration of the response, median survival and time to progression, it is very difficult to know exactly what the numbers will be. The Phase III trial is precisely defined in terms of the patient population, i.e., first-time recurrent glioblastoma. This is important in light of the fact that other brain cancers have different responses to therapies and hence different outcomes with respect to progression and survival which can skew or confuse results.

The comparison with temozolomide (Temodar) is appropriate since studies are starting to indicate that chemotherapy with multiple agents is no better than the use of Temodar alone (oral administration, usually about 150-200 mg/m2 for 5 days on a monthly cycle). Actually, the data for a Phase II study of Temodar in patients with first recurrent glioblastoma is published and indicates a progression-free survival at 6 months of 18%; median progression-free survival of 9 weeks and median overall survival of 22 weeks. A very low complete response rate was observed (less than 10%) and stable disease was noted in about 45% of the patients. The safety profile was similar to that described for Cotara. There is a good literature on what can be anticipated for the treatment of these patients with Temodar.

Recurrent glioblastoma is a terrible, fast growing lesion that invades and recurs in patterns that can be unmanageable. The survival rate and time is extremely poor. We wish the patients the best of success.

Editorial comment: I would have titled today's PR something like, "Peregrine Pharmaceuticals Announces the Design of the Fast Track Phase III Study for Brain Cancer Approved by the FDA".

Of course, we wait on the designation of the trial centers, how fast Europe and Canada can come on board and the expected accrual rate of patients. Unfortunately, it will be a quick read-out, since this particular cancer is so devastating.

 

01/09/2002

Oncolym remains somewhat of a mystery to me with respect to status of trials and exactly how it will be used in NHL. Nearly 60 patients were treated with I-131 labeled Lym-1 antibody between 1985 and 1994 (Clin Can Res 3: 1253, 1997). The Lym-1 antibody targets a mutated HLA-DR antigen found on B-cell lymphomas (patients must be positive for the presence of this antigen to enter this form of therapy). Interestingly, a lot of the dosimetry measurements (radioactivity found in normal tissue) and biodistribution did not really predict for response in the patients, but half-life of the radioisotope was an important predictive parameter. At the same time, the development of anti-mouse antibodies (the Lym-1 antibody is a mouse hybridoma antibody) did correlate with improved survival, suggesting that development of these antibodies by patients, thought to present an obstacle to therapy (and can) actually may improve the therapeutic benefit of Lym-1 therapy.

The DeNardos championed the use of Lym-1 therapy over the past decade and published many papers on the use and comparison of radiolabels for this antibody (more on these comparisons later). Early studies using I-131 Lym-1 indicated that responders had a median survival of about 84 weeks, compared to 22 weeks observed for non-responders (Cancer 80: 2706, 1997).

 

Early 1998, PPHM announced the start of a Phase II/III trial of Oncolym in treatment of intermediate- and high-grade refractory or relapsed NHL. This trial was to evaluate he therapeutic efficacy of two doses of 60 mCi/m2 (about 120 mCi per patient) given 6 weeks apart.
At ASCO in 1998, a retrospective analysis of this therapy was presented by Jamie Oliver and the DeNardos. A limited number of patients were used for this analysis. It was observed that response was dose-dependent (the higher the dose of radiation, the better response rate and durability of that response) and repeated dosing was superior. At the same meeting, dosimetry results were given by the multi-center group (Iowa, M.D. Anderson, Miami, Cornell, George Washing U). They again spoke of improved responses with subsequent doses of antibody-delivered I-131. Similar results were presented the summer of 1998 by the Georgetown U group at a Nuclear Medicine meeting in Toronto. The treatment protocol was amended that summer by PPHM (with permission of the FDA) to include patients that actually failed prior therapy with monoclonal antibodies (presumably patients that had failed Rituxan or Bexxar?), but I have not found publications on the success or failure of these specific patients treated with Oncolym. Actually, one can not find a formal publication at all using the name Oncolym. Strange.

 

However, the DeNardos remained prolific and productive in their use of the Lym-1 antibody. They started studies using fractionated doses of Lym-1 coupled to the 67Cu isotope by a methodology that allowed binding of the copper atom to the antibody. This method was different than the chloramine-T method commonly used for iodine (131) coupling to the Lym-1 antibody. Now, radiometal labeled antibodies provide a higher tumor radiation dose than corresponding I-131 labeled antibodies. This by itself doesn't mean much, unless you look at how long the radiation stays at the tumor site…then it becomes important. In other words, one can always up the dose of I-131, but the question is what is damage to normal tissue and bone marrow and how long is the isotope in the vicinity of the tumor. They described the use of 67Cu-Lym-1 in NHL using a minimum of 2, and up to 4, doses (Anticancer Res 18:2779, 1998). They concluded in this study that the isotope 67Cu gave good imaging, favorable dosimetry and a high ratio of tumor to marrow radiation (good). Immediately after that publication, in the summer of 1998, they published a similar study with I-131 Lym-1 with multiple dosing up to a total of 300 mCi over the course of several weeks. Tumor regression occurred in 83% of the patients, and was prolonged enough in 57% of the patients to qualify them as responders (Cancer Biother Radiopharm 13: 239, 1998). In the Fall of 1998, they published a study about I-131 Lym-1 therapy describing the maximum tolerated dose & efficacy for fractionated multiple dose therapy of NHL (J Clin Oncol 16: 3264, 1998). Ten of 14 patients who received at least two doses of therapy and 11/21 total entries responded. Seven of the responses were complete with a mean duration of 14 months. All responders had at least a partial remission after the first therapy dose, suggesting that response after initial dosing was predictive for subsequent treatment response. A similar report was published in 1999 (J Nucl Med 40: 302) using 67Cu with superficial lesions of NHL and they achieved about a 50% regression of measured tumors. The remarkable thing about use of the 67Cu isotope was the long residence time of the radiation within the tumor and that even imaging (subtherapeutic) doses showed some regression.

 

They then published (a study) (Clin Can Res 5: 533, 1999) where they compared the pharmacokinetics and dosimetry in patients with NHL using either I-131- or 67Cu-labeled Lym-1 and concluded that due to the better ratio of tumor/normal tissue delivery of isotope, lower radiation to the bone marrow by 67Cu and imaging was improved using 67Cu that the use of 67Cu may be superior to I-131 for Lym-1. Yes, I read the paper in its entirety. They do mention that 67Cu is not routinely available, is expensive and would require a ramp-up of accelerator facilities not readily available. Several subsequent publications review the dosimetry and parameters associated with Lym-1 therapy (using either 67Cu or I-131; J. Nucl Med 40: 2014, 1999; Clin Can Res 5: 3330s, 1999); J Nucl Med 40: 1317, 1999).

Now the company PR of March 2000 gives a rationale for re-evaluation of Oncolym in a Phase I setting. Bonfiglio stated that a three treatment dose protocol was cumbersome, expensive and had difficulty in recruiting patients. And he stated that an analysis of the data revealed that 80% of the patients treated with a therapeutic dose of Oncolym responded well to the first dose. I assume he is referring to those that go on to be responders as found in the earlier studies. The status of the trials remains somewhat unclear to me. We do list many centers that are open for enrollment. From a purely scientific point of view, I would still wonder whether optimal treatment requires multiple doses and the fact that other radiolabel therapies for NHL, such as Zevalin (yttrium90 isotope) and Bexxar (I-131) use multiple dosing.

 

01/29/2002

This anti-VEGF subject is a little too complex for me. Let me explain. VEGF has long been known to be a growth factor that is involved in myriad of embryonic, adult tissue maintenance and tumor growth and vascularization events. There are several VEGF receptors (VEGFR) found on different tissues, some fairly specific, such as the VEGFR2 (KDR/Flt-1) found on vascular endothelium, although this receptor is important in embryonic development (Proc Natl Acad Sci U S A 1997 May 13;94(10):5141-6, "Ligand-dependent development of the endothelial and hemopoietic lineages from embryonic mesodermal cells expressing vascular endothelial growth factor receptor 2", Eichmann A, Corbel C, Nataf V, Vaigot P, Breant C, Le Douarin NM). However, this receptor is pretty specific for tumor vasculature and hence an attractive target for antiangiogenic therapy.

There are currently several approaches to anti-VEGF therapy, e.g., blocking the binding of VEGF itself to receptors (a rather risky non-specific issue, due to need for VEGF in normal tissue function), and the blocking of binding of VEGF to tumor cell receptors (tumors use and secrete VEGF in large quantities) by the use of antibodies (Genentech and IMCL). In addition, other strategies have attempted to specifically block the phosphorylation of these receptors, since they have function that is known as tyrosine kinases (the SUGEN compounds, 5416 and 6668, and Novartis PTK787). Hence, there is little doubt that the more one can successfully target the tumor endothelium carrying the KDR receptor, the more superior the therapy becomes. As an example, the VEGFR-2 has been found in 90% of tumor specimens of head and neck cancer (Neuchrist C, et al., Laryngoscope 2001, lll: 1834) and appeared to be localized to vascular endothelium. This has been observed in many solid tumors and also by Thorpe and his colleagues (J Control Release 2001 Jul 6;741-3):173-81, "VEGF-VEGF receptor complexes as markers of tumor vascular endothelium.", Brekken RA, Thorpe PE) as well as expression of the VEGFR-2 in vasculature of VEGF-secreting tumors ( Feng, D., Nagy, J.A., Brekken, R.A., Pettersson, A., Manseau, E.J., Pyne, K., Mulligan, R., Brekken, R., Thorpe, P.E., Dvorak, H.F., & Dvorak, A.M. (2000) Ultrastructural localization of the Vascular Permeability Factor/Vascular Endothelial Growth Factor (VPF/VEGF) Receptor-2 (FLK-1, KDR) in normal mouse kidney and in hyperpermeable vessels induced by VPF/VEGF-secreting tumors and adenoviral vectors. J. Histochem. Cytochem., 48:545-555).

 

Scientists from Imclone reported several years ago the value of blocking the VEGFR-2 receptor using the DC101 antibody in mice (Cancer Metastasis Rev 1998 Jun;17(2):155-61, "Monoclonal antibodies targeting the VEGF receptor-2 (Flk1/KDR) as an anti-angiogenic therapeutic strategy", Witte L, Hicklin DJ, Zhu Z, Pytowski B, Kotanides H, Rockwell P, Bohlen P). These studies evolved into the clinical trials of their anti-VEGF/KDR receptor antibody, IMC-1C11. In May, 1998, IMCL was awarded US Patent 5747651 on the use of antibodies against the extracellular portion of the Flk-1/KDR receptor of VEGF. Early last year, the Imclone scientists reported the ability to select high affinity antibody construction against VEGFR-2 by the use of phage-display technology (Int J Cancer 2002 Jan 20;97(3):393-9, "Selection of high affinity human neutralizing antibodies to VEGFR2 from a large antibody phage display library for antiangiogenesis therapy; Lu D, Jimenez X, Zhang H, Bohlen P, Witte L, Zhu Z).

The highly specific antibody, described by Thorpe, 2C3, has been shown to have potent antitumor activity, presumably by targeting the tumor endothelium (Brekken, R.A., Overholser, J.P., Stasny, V.A., Waltenberger, J., Minna, J.D., and Thorpe, P.E. (2000) Selective inhibition of VEGFR2 activity by a monoclonal anti-VEGF antibody blocks tumor growth in mice. Cancer Res., 60, 5117-24). Now, the present patents awarded to Thorpe, and I guess, subsequently assigned to PPHM covers the usual infinite scope of applications that only Thorpe can envision and articulate, even to the point of delivery of about every diagnostic and therapeutic agent ever used or being tested (including angiostatin, endostatin, etc). There seems little doubt that the specificity of such delivery may exist (what happened to the SUPERGEN studies with VEGF-trojan horse?) but this enthusiasm needs to be tempered with the reality of PPHM activities.

First, these studies appear to be preclinical, i.e., promising due to the observations using good animal tumor models. One of the most exasperating observations about this company is the inability to get the Thorpe science into the clinic. We have had VTA in several forms; such as targeting expressed and induced receptors on tumor endothelium, the delivery of either conjugated or free truncated tissue factor and the potential antitumor activity associated with antibodies that target phosphatidylserine on tumor endothelium (Ran, S., Rote, N., and Thorpe, P E. Phosphatidylserine is a marker of tumor vasculature and a potential target for anti-cancer drugs; submitted). However we jockey for position with ARCUS (and OXGN) on who owns what in what form (conjugated/non-conjugated), it is time to get some of these molecules into the clinic. We can't do them all. They all can't be the best. Somebody has to decide what to develop in terms of endothelial cell targeting, study the parameters within the confines of good animal models and quickly get into Phase I trials that can confirm the biodistribution, activity and behavior of the agent in patients.

 

An infinite patent package of pipelines that are never tested doesn't do anybody any good. So, in this regard, I am still focused upon the activities of the company that give credibility to the products under development, mainly Cotara and Oncolym.

 

In that regard, guess I might as well make a few more comments.
1. Oncolym. What a disaster of such a promising molecule. Fascinating trials could have been formulated regarding therapy of relapsed lymphoma (every therapy requiring of course, a strong expression of the HLA-DR10 antigen by lymphoma cells, but that is easily assayed). I am not sure we ever came away with a strong indication for optimal dose and scheduling for I131-Lym1 and yet the company says that strong analysis of the data indicate that a one-dose scheme should be developed. It really doesn't matter what I think, but the publications by the DeNardos clearly indicated that the durability and depth of response was dose-dependent (several treatments). I doubt we can deliver that accumulated radiation by a single dose, at least using I-131. And of course, now there is evidence that the Cu67 isotope may have preferable properties. We have no real word of the status of the Phase I trials using single-dose methods even though the web site says multi-center trials. I doubt the enrollment is robust. The front line therapies will be rapidly changing in most cancers and with the lessons learned by Bexaar, Rituxan and Zevalin (although the FDA is giving these therapies a rough time; the C225 antibody of IMCL is very good therapy when combined with conventional cytotoxics), it just appears we make little progress in the clinic with Oncolym. There could be several indications for the use of Oncolym, regarding combination therapy or studies to determine the development of resistance to Oncolym (loss of the target antigen, which is not unique to antibody-mediated therapies, e.g., Gleevec (STI571, the tryosine kinase inhibitor of the PDGF-receptor in CML now has resistance based upon cells that mutate and overexpress that receptor and become resistant to Gleevec). Except for the published literature by the DeNardos, there is nothing about "standard" Oncolym therapy in the medical literature. Certainly no update has been given by the company….that I recall even in enrolling or treating the first patient in this new Phase I trial. Where the funding comes from for the Oncolym trials is unknown, since we know the bulk of monies are directed to the ongoing Phase II and to-start Phase III of Cotara.

2. Cotara. Clinically, the orphan-status of this agent doesn't mean anything, and the Fast-Trac of Phase III means a lot. The number of experimental therapies for glioblastoma is enormous, considering the relative small numbers of patients with this disease compared to mainline cancers, such as prostate, breast and colon. It is interesting that the FDA leaned toward a comparative study with temozolomide, which suggests that this form of chemo is approaching front-line therapy for recurrent glioblastoma. However, the use of the chemo-wafers, and now small-molecule development (cytokines, tyrosine kinase inhibitors), as well as other targeting antigens for antibody-mediated therapy (such as the Bigner group) may be improved with better delivery methods. And, we know this Phase III trial will be very, very expensive, especially if we conduct the trial in Canada and Europe as well as here in the U.S.A. Certainly this clinical use of Cotara is the actual leading candidate for product-income over the next few years. How the Phase III (or ongoing Phase II) trials will integrate the collaboration with Image-Guided Neurologics in their use of the Navigus Array Catheter remains to be presented.

 

I remain quite disturbed about the lack of formal publications regarding any case studies involving Cotara in brain tumors (case studies are interesting, informative and rapid ways to tell how a field is developing in new therapies). There must be little motivation or incentive for this Assistant Professor to publish these findings which is extremely unusual for a young clinician in academic medicine. I assume we will have something new to say at ASCO, and it is disturbing that Cotara therapy of brain cancer is NOT well known to the neuro-oncology community and doesn't find it way to a podium setting at a meeting. As I have mentioned in the past, poster sessions do not necessarily reflect unenthusiasm for a research presentation, (many high-profile results of other biotechs are presented in poster sessions), but ultimately the HOT topics of a field find their way to a podium presentation.

3. Cotara in solid tumors. Multi-site studies at good medical settings, yes, and again, we have no reports at all concerning the enrollment or findings of the Phase I trials in solid tumors with Cotara, other than last years paltry data from Mexico. Yes, I know that Phase I trials are designed to determine maximum tolerated dose, pharmacokinetics (distribution), localization ratios of isotope to tumor/normal tissues and other parameters, but we have really no clue as to the progress of these trials. I guess that is the disturbing part…progress. We really don't seem to know about progress. There are so many ways for a company to let the shareholders know that their compounds and drugs are moving along a track, e.g., seminars, small conferences, society meetings, and brief publications.

Now, the China SDA approval of chTNT for certain indications (I still emphasize the probable need for an intratumoral protocol, besides IV injection) will be overwhelming validation for at least considering the odds of Cotara being a player in therapy of solid tumors. The transition needed from these data out of China should be rapid and smooth into the trials of Cotara in this country (yet, to my knowledge, we have no lung cancer trials ongoing, which is surprising given the modest amount of data known from China). There seems little doubt that short-term sentiment about the value of the Cotara therapy will be established by what China SDA does. As I mentioned before, the link to the China data (which I can not seem to resurrect stated that approval was on track for May, 2002).

 

4. ARCUS. Oh well, that seems a somewhat distant cause. Unless OXGN really wants to try targeting the tubulin-binding agents (combretastatin derivatives) using TNT-type antibodies, it seems we are intent are using un-conjugated VTA agents on our own. The Thorpe anti-PS stuff is truly frustrating and must be to him also. He has submitted a paper on the targeting of PS (according to the PPHM website). It seems clear, IMO, that the anti-PS will be developed via ARCUS, since that is where the patent was awarded. We really don't know what has happened to the truncated-tissue factor stuff. ARCUS remains a mystery to me…even more so than the SUPG deal with the VEGF-gelonin molecule developed by M. Rosenblum.

5. Oakwood Labs: This company develops delivery of compounds and drugs via liposomes and obviously believe they can improve their targeting with TNT-guided delivery to the tumor bed by coupling the antibody to liposomes that contain toxic goodies. This will take some preclinical studies on animal tumor models, doses, coupling procedures that are optimal and scheduling parameters. Nothing coming soon here that I can see. But that's okay. A pipeline development.

6. Merck (Lexigen): This licensing/collaboration with Lexigen probably centers around the fusion-peptide technology of TNT-IL-2 (Epstein has published on this concept, (Pretreatment with a monoclonal antibody/interleukin-2 fusion protein directed against DNA enhances the delivery of therapeutic molecules to solid tumors. Clin Cancer Res. 1999 Jan;5(1):51-60). As I mentioned before, this methodology probably has been secured by S. Gillis, a recognized world-class researcher in the area of immunocytokine peptides and Gillis is the head of Lexigen. I note that the agreement was over a year ago, which means the discussions of this agreement were probably at least six months before that…and in the year and a half since, no new data is in the literature that shares a Lexigen/PPHM byline, although Gillis has published recent papers on the use of the fusion peptide-IL-2 effects ("Improved circulating half-life and efficacy of an antibody-interleukin 2 immunocytokine based on reduced intracellular proteolysis." Clin Cancer Res. 2002 8: 210-216; as well as "Augmentation of antitumor activity of an antibody-interleukin 2 immunocytokine with chemotherapeutic agents." Clin Cancer Res. 2001 Sep;7(9):2862-9.) I assume some sort of preclinical studies are underway in this area. How this fits into the overall VEA scheme of PPHM is not clear to me.

7. AVID. Well, all of us know what is trying to happen there. We wait.

I do applaud the very hard work and enthusiasm of Ed L. but I also believe there are legitimate (and non-shallow) ways for the company to show us that science and business is progressing in ways that he has not done. He needs to get his clinicians publishing studies and working their way into podium sessions, attending more high-profile small conferences (which is the way of biotech lately, the AACR conferences for example) and hitting all the clinical meetings.

 

02/01/02

You ask, "Do any of you longs which know this company inside out...know what EL's agenda is to promote the China data? Has EL assembled a crew of top Ph.Ds/Oncologists to decipher these clinical trials? Is it your opinion Medipharm will let us publish this data to support our cancer therapy? Does anyone have a grasp on what will happen once we get the China data?"

I can not speak for Mr. Legere at all, but I would emphasize that the China data does not belong to PPHM. It is property of Medipharm and their collaborators (presumably the Epstein company). We are involved for two important reasons, (a) we have the ability to manufacture the radiolabel antibody and share royalties, but more importantly, (b) the success of the China trials have a huge impact on validating the Cotara-based therapy. This is what is most important to me. I have no idea what China data he has viewed. The translated abstract of a couple months ago is the only data I am aware of and it certainly seemed very encouraging with respect to lung cancer and intratumoral infusion.

You also stated, "When I see EL promoting the mab plant, and not the data we have from Phase II, it makes me wonder why we are focusing so much attention on the mab facility. I like the idea of Big Pharma looking at our data and paying for our trials." In my opinion, Mr. Legere is focusing upon immediate goals under his control, such as revenue obtained from contracts of Mab manufacture. I often complain about the lack of peer-review publication and visibility of the Cotara-glioma results. Of course, having Big Pharma examining the data and funding the trials does have the cost of "diluting and sharing" any subsequent revenue.

To me, the biggest benefit of actually knowing the China data is the immediate decisions about what strategies of Cotara work and don't work, with regard to tumor type, location and tumor burden. If I knew the China data obtained with many tumor types, I would focus upon the success and discard the failed approaches, all techniques, doses and delivery methodology being equal. I do believe that Mr. Legere is doing his best with all the resources available to him.

 

02/01/02

You ask an important question, wondering how the China data will be utilized for PPHM. I believe there are several features of the "business" and the "science" of Cotara that are crucial for the company. First, there is the example that T. Chew successfully negotiated the regulatory obstacles for Fast Trac evaluation of Cotara in recurrent glioblastoma and he has successfully brought a product through the FDA in his prior work. This is encouraging. So, one could feel confident that Chew can assemble the data for the FDA when it is presented in a format that can be evaluated and summarized. Will PPHM have the "task force" available to evaluate the China data? Several avenues are available. First, he has the principal investigators of the multi-center glioma trials to evaluate the findings of intratumoral infusion of Cotara in solid tumors. In addition the company has the resources of the principal investigators of Cotara in other solid tumors (Stanford and the Mayo Clinic). I may be somewhat simplistic but the results of China will be, in my opinion, straight-forward, assuming the methods and measurements of the use of Cotara in China have been controlled.

Remember, the trials of Cotara in solid tumors here in the USA are Phase I, designed to study toxicity and pharmacokinetics and NOT efficacy. Presumably, we know quite a bit from the Mexico studies. However, the China data should outline pure success and failure and in a variety of tumor types. Assuming their procedures are carefully designed and controlled, the data should be invaluable in determining the course of studies here in the USA about Cotara. Through the expertise of Epstein, I would also think that the company has the resources to review the data and utilize it to its fullest extent. . The China data should guide our use of Cotara in solid tumors. This requires that the China data is simple enough in the parameters of the trials (type of tumor, patient selection, amount and frequency of TNT administered, route of administration, close follow up of clinical course of disease, influence of prior therapies, subsequent observations of extent and site of recurrent disease, and observed toxicities).

In this regard, the track record is not encouraging. The example using Oncolym is dismal. We went from the clinical use of Oncolym via the DeNardos and should have entered into pivotal (final) trials in lymphoma and ended up going backward to Phase I with Schering, based upon "outside" opinion that one-dose protocols should be developed (in spite of the published data), and the status of Oncolym appears uncertain. I have never understood exactly where the wheels came off in the Oncolym "business".

The personnel to the Mab facility are technical support and staff associated with manufacture of monoclonal antibodies and the regulatory requirements of their production and not personnel associated with research and development of clinical trials. The R & D of PPHM is Epstein and Thorpe and their labs are supported by funds from PPHM.

 

02/10/02   #390

The decision to stop the (Sugen) trials involving the tyrosine kinase inhibitor (RTKi) SU5416 was disappointing in light of the promise of this form of therapy. As late as last year at ASCO, this form of therapy was obtaining some meaningful responses in patients when used with chemotherapy. It is entirely possible that the parameters that ultimately determine patient responses to two-compartment targeting may be lost when trials are performed on "all comers" or large groups of patients that have seemingly homogeneous conditions (metastatic colon carcinoma with refractory disease) yet very heterogeneous responses that almost ruin any statistical analysis for that group. The SU5416-chemotherapy trial had some very dramatic responses that got lost in the final analysis; and I know this is what Rosen is talking about in "learning" from this type of trial.

Modern concepts of cancer therapy has focused upon two-compartment targeting; the tumor cell themselves and tumor-associated blood vessels. The strategies for this concept vary widely. Sugen originally targeted growth factor receptors thought to be needed for proliferating tumor cells as well as endothelial cells (such as epidermal growth factor, EGF; vascular endothelial growth factor, VEGF; basic fibroblast growth factor; bFGF and platelet-derived growth factor, PDGF). Different companies are attempting to target specific properties of tumor-associated blood vessels that may be unique to dividing (and forming) vasculature within an expanding mass of tumor (VTA by Thorpe [via expression of phosphatidylserine or VCAM-1 using truncated tissue factor], combretastatin by OXGN, TNP-40, endostatin, angiostatin by ENMD, VEGF-gelonin presumably by SUPG and a myriad of other molecules that have indirect effects on endothelial cells.

02/10/02   #391 

The optimal result of two-compartment therapy will be obtained when the tumor has induced the coordinate receptor on the endothelium for a growth factor they both secrete and express the receptor (best example is the large secretion of TGF-alpha from tumor cells that upregulate the EGF-receptor on endothelium in addition to those expressed on the tumor cells themselves). In theory, this type of tumor will be very sensitive to targeting the EGF-receptor (such as PKI-166 by Novartis, or the IMCL C225) and if one could determine prior to therapy that the tumor is secreting TGF-alpha (the most common ligand for EGF-r) and that the tumor is expressing the EGF-r as well as the tumor blood vessels, the odds of successful therapy (at least using that form of therapy) go up tremendously and the patients can be divided into groups that have certain "markers" that may be amenable to certain targeting agents (such as RTK-inhibitors). This is being pursued vigorously in preclinical models (and can be found in the literature).

At the same time, we are recognizing that tumor-associated endothelial cells, often thought to be the immutable target for direct antiangiogenic therapy has properties that can be "conferred" by tumor cells that may cause resistance to apoptotic-inducing agents. This property of having resistance induced by factors secreted by tumor cells (instead of classical selection as found in those cells that survive a round of chemotherapy) may cause problems in formulations of two-compartment targeting. But the SUxxxx compounds have pioneered a very important concept that has lead to a much better understanding of the molecular description of what drives the proliferation of tumor cells, causes the continual formation of new vasculature, confers protection upon these cells and thwarts direct and indirect targeting of these molecular pathways.

 

Date:  Wed Mar 13, 2002  12:27 pm

 

It is completely unacceptable that physicians running the clinical trials for PPHM Cotara did not submit presentations to ASCO, the premier clinical oncology meeting in the world. Phase II data was presented a year ago (May 2001) at ASCO and there has been a year follow up in that data. In addition, we agreed to examine the use of the Navigus array catheter (Aug 2001), certainly there is "new" data about this device i.e., distribution of antibody, localization images, etc that would have made a nice presentation.

Patel and his multi-center colleagues should have published a manuscript on interim Phase II Cotara by now. Obviously the findings are encouraging enough to warrant Fast Track consideration by the FDA using a comparative study with chemotherapy in glioblastoma. There must have been interesting findings that would have made a nice case study report (which is common in medicine).

It has been nearly 15 months since the first colorectal patient was treated at Stanford with Cotara and almost a year since the other solid tumor trials at Stanford and Mayo were started. Nothing has been presented regarding these Phase I trials and ASCO would be the place to start. The absolute dogma of academic medicine is to publish and present data.

It seems paradoxical that Thorpe and Epstein have published for years in preclinical models of VTA and VEA, yet nothing is in the clinic (while) the clinical studies for Cotara have been going on for years and nothing gets published.

 

Date:  Fri Mar 15, 2002  6:30 am
Subject:  Epstein and Thorpe at AACR

 

LEC/chTNT-3 fusion protein for the immunotherapy of solid tumors

 

Jiali Li, Peisheng Hu, Leslie Khawli, Alan Epstein, University of Southern California, Keck School of Medicine, Los Angeles, CA.

The human chemokine LEC (liver-expression chemokine), also named HCC-4, NCC-4 and LMC, was originally found in an expressed sequence tag library and later the gene was located on chromosome 17q in the CC chemokine gene cluster. LEC has been shown to chemoattract both monocytes and lymphocytes mediated by interacting with CCR1 and CCR8, but not neutrophils. In this study, a LEC/chTNT-3 fusion protein has been generated to target this potent chemokine to tumors in order to generate an effective immune response. The cDNA of LEC has been cloned by RT-PCR from Hep-2 cells. Because the N-terminal of chemokines are important for their activity, we fused the C-terminal of LEC with the N-terminal of chTNT-3 heavy chain variable region with restriction enzymes Xba1 and Not1 and then the fused LEC/chTNT-3 heavy chain was inserted into a glutamine synthase gene amplification system expression vector pEE12 with an antibody leader sequence. The chTNT-3 light chain was carried by another vector pEE6 and co-transfected into the murine myeloma cell line NS0. The fusion protein was purified by tandem protein-A affinity and ion-exchange chromatography. The proper assembling of the fusion protein was demonstrated by SDS-PAGE which showed a 68KD band compared with a 56KD for chTNT-3 heavy chain under reduced conditions. The bioactivity of the fusion protein was demonstrated by a chemotasis assay using the human monocyte cell line, THP-1 and compared with recombinant LEC. The immunoreactivity of the fusion protein was determined by binding to fixed Raji lymphoma cells. These binding studies showed that linking the chemokine to the variable region of the antibody does not interfere with antigen binding under physiologic conditions. Furthermore, LEC/chTNT-3 retains its chemokine chemotasis functionality. In vivo immunotherapy studies will focus on the recruitment of immune effector cells to tumors and on monitoring tumor growth in mice receiving different regimens.

 

 

Humanization and mutation of an anti-nuclear antibody developed for human cancer therapy

Jianghua Yan, Peisheng Hu, Leslie A. Khawli, Alan L. Epstein,
Department of Pathology, University of Southern California School of
Medicine, Los Angeles, CA.


Tumor Necrosis Treatment monoclonal antibody (TNT-3) was developed by our laboratory to target necrotic regions of solid tumors. As a carrier of radionuclides and immune modulators, chTNT-3 has been shown to be a promising targeting agent for the radio- and immunotherapy of solid tumors in animal models and man. To improve its clinical potential, a humanized TNT-3 was designed and constructed by searching human anti-DNA antibody data bases and using PCR assemblage. To restore and improve the affinity of huTNT-3 candidates, CDR3 of huTNT-3 heavy chain genes was simultaneously mutated by site-specific random mutation. Reconstructed scFv of huTNT-3 were inserted into the Lambda phage SurfZAP vector and displayed on the surface of phage. Ten mutants were selected by four rounds of panning against crude DNA. The light and heavy chains were then reconstructed in pEE6 and pEE12 vectors, respectively, for expression of whole antibody in NSO cells using the glutamine synthase expression system. Binding studies against crude DNA demonstrated that eight of the mutants had a 2-8 fold improvement in affinity compared to chTNT-3 while two mutants had a 1-4 fold weaker affinity. Analysis of the mutants with improved binding characteristics showed that positively charged amino acids such as Arg and His replaced existing residues in four of the mutants while the other three mutants showed replacement with amino acids containing hydroxyl groups. In one exceptional case, the replacement of Arg with Leu increased binding activity by four fold. These results suggest that changes in the electrostatic or hydrogen –bonding potential of residues contributed to the observed improvement in antibody binding to crude DNA antigen. The availability of a high affinity humanized TNT-3 reagent will facilitate the development of clinically relevant
reagents useful for the therapy of solid tumors in man.

 

 

Comparison of three different targeted tissue factor fusion proteins for inducing tumor vessel thrombosis

Peisheng Hu, Jianghua Yan, Leslie Khawli, Thomas Bai, Jahangir
Sharifi, Alan Epstein, University of Southern California, Los Angeles, CA.


Tissue Factor is a cell membrane receptor protein that is the initiator of the extrinsic pathway of the blood coagulation cascade and is normally released from damaged tissues. By substituting the attachment site with a tumor delivery agent, this potent thrombogenic protein in its truncated form can be targeted to the tumor where it can initiate clotting thereby occluding the tumor's blood supply to cause rapid and massive cell death. In this study, we have explored three different delivery systems, namely, chTNT-3, which targets necrotic regions of tumors, chTV-1, which binds an exposed constituent of the tumor vessel basement membrane, and a RGD motif which targets tumor vessel endothelial integrins on the luminal side of the vessel. The resultant recombinant fusion proteins, chTNT-3/tTF, chTV-1/tTF, and RGD/tTF were expressed either in NSO cells using the glutamine synthase expression system or, as in the case of the RGD reagent, in E. coli. Antigen binding studies were performed to demonstrate retention of the binding activity of the antibody moiety and clotting studies revealed potent activity of the Tissue Factor constituent of the fusion proteins. After intravenous injection in MAD 109 lung carcinoma-bearing BALB/c mice, histological analysis revealed that all three reagents induced microregional thrombosis and subsequent necrosis in tumors. Of interest, the chTV-1/tTF and the RGD/tTF fusion proteins induced thrombosis in small and medium sized tumor vessels while the chTNT-3/tTF induced clotting in larger vessels. These studies demonstrate that multiple targets exist which can be used to localize truncated Tissue Factor to occlude tumor vessels in this mouse tumor model. Further experiments are underway to explore additional target sites, which may be more efficient and/or specific for the delivery of truncated Tissue Factor in order to identify a single reagent, which can be used in experimental therapeutic studies in man.

 

 

Characterization of antigens recognized by chimeric Tumor Necrosis Treatment anti-nuclear monoclonal antibodies

Meg L. Flanagan, Jianghua Yan, Peisheng Hu, Alan L. Epstein, University of Southern California Keck School of Medicine, Los Angeles, CA.

Our laboratory has developed a panel of anti-nuclear monoclonal antibodies for targeting necrotic regions of solid tumors. This panel includes three chimeric monoclonal antibodies (chTNT-1, -2, -3) and a phage display-generated human monoclonal antibody (NHS76) generated against the same antigen as chTNT-1. To characterize the antigenic binding sites of these reagents, ELISA studies were conducted using various nuclear antigens, including crude DNA, single- and double-stranded 25bp DNA oligonucleotides, total cellular RNA, and histone subunits H1, H2a, H2b, and H4. In response to reports of charged-based affinity of anti-DNA antibodies for glycosaminoglycans of the extracellular matrix, we also used chondroitin sulfate, heparin sulfate, and hyaluronic acid as potential antigens. From these ELISA we found that chTNT-2 binds histone but none of the nucleic acid or glycosaminoglycan species tested, whereas chTNT-3 and NHS76 bind both crude DNA and histone. chTNT-2, which has been previously shown by immunogold electron microscopy studies performed in our laboratory to bind heterochromatin, may have additional uses as a targeting vehicle. Interestingly, chTNT-3 and NHS76 both bound crude DNA and histone, demonstrating that these MAbs may bind similar epitopes on nucleosomal complexes. chTNT-1 also bound crude DNA and histone as expected, but exhibited binding to several other species as well. It may be that chTNT-1, which is currently showing promise in a number of clinical trials for the radioimmunotherapy of solid tumors, exhibits this promiscuity due to its known high isoelectric point. In the future we plan to examine in greater detail the localization of these antibodies by confocal microscopy and, where possible, use surface plasmon resonance technology to examine the kinetics governing the binding relationships between our TNT MAbs and their antigens.

 

 

In vitro and animal model studies of VEGF121/rGel fusion toxin effects on breast cancer cells

Khalid A. Mohamedali, Lawrence H. Cheung, Sophia Ran, Philip Thorpe, Michael G. Rosenblum, M.D. Anderson Cancer Center, Houston, TX; U.T. Southwestern, Dallas, TX.

The angiogenic factor VEGF121 fused with the recombinant plant toxin gelonin (rGel) exhibits potent cytotoxicity towards tumor neovasculature and inhibits tumor growth by virtue of its selective targeting of tumor vessels. We have used in vitro and animal models to further understand the mode of action of VEGF/rGel on tumor cells in vivo. Preliminary studies have suggested that interruption of blood flow to tumors with agents targeting tumor vasculature generates intratumoral hypoxia and concomitant changes in the surrounding pH. Vascular endothelial cells over-expressing flk-1 (PAE/flk-1) were treated with an IC50 dose of VEGF/rGel for 24, 48 and 72 hours. At the appropriate timepoints treated and control cells were harvested and the effect of VEGF/rGel on intracellular events was examined by extraction of mRNA and microarray analysis of proteins involved in signal transduction, stress response, cell cycle control, hypoxia and metastasis. To examine the effect of VEGF/rGel on tumor cells, MDA-MB-231 breast cancer tumor cells were co-cultured with PAE/flk-1 with the two cell lines separated by a thin membrane, allowing exchange of nutrients. The endothelial cells were treated with various doses of VEGF/rGel and the effect on MDA-MB-231 cells was examined visually after 72 hours. PAE/flk-1 cells in the upper chamber were treated with an IC50 dose of VEGF-rGel over 72 hours after which both control and treated PAE/flk-1 and MDA-MB231 cells were harvested, RNA extracted and subjected to microarray analysis. We repeated the above experiment and incubated the cells under hypoxic conditions to examine genetic changes associated with hypoxic stress. These results are under analysis and will be reported. Internalization of VEGF-rGel into PAE/flk-1 cells was also investigated 1 hr, 2hr, 10 hr, 16 hr and 24 hrs after treating with VEGF-rGel. VEGF-rGel was detected by both anti-VEGF and anti-rGel antibodies using immunofluorescence, and suggests internalization within one hour of incubation. Finally, the plasma clearance and tissue distribution of VEGF-rGel in tumor-bearing mice was examined. Nude mice bearing orthotopic MDA-MB231 tumors were injected with 1 ìCi of 125I-labeled VEGF-rGel and tissue distribution and plasma clearance was assessed 24, 48 and 72 hrs post injection. Research conducted, in part, by the Clayton Foundation for Research.

 

 

Angiopoietin-2 transfection does not enhance the sensitivity of the NCI-H358 lung tumor to VEGF-neutralizing therapy


Xianming Huang, Sophia Ran, Chelsea Swandal, Joanna Brochu, Mary Bennett, Philip Thorpe, UT Southwestern Medical Center at Dallas, Dallas, TX.

Angiopoietin 2 (Ang-2) is an angiogenic factor that might coordinate with vascular endothelial cell growth factor (VEGF) in the modulation of angiogenesis. It has been suggested that, in the presence of VEGF, Ang-2 induces angiogenesis, but, in the absence of VEGF, it induces vessel regression. In the present study, we examined the complementary and coordinate action of Ang-2 and VEGF in tumor growth and angiogenesis. Human non-small cell lung carcinoma NCI-H358 cells were stably transfected with Ang-2. In vitro, the Ang-2 transfected cells grew at the same rate as did tumor cells transfected with empty vector. However, they grew significantly faster as tumors in mice than did mock transfected tumor cells and had higher proliferation indices, as judged by PCNA staining. Ang-2 transfected tumors had aberrant vessels: they grew as dense nests of tumor cells that possessed few microvessels surrounded by large sinusoid-like vessels. Treatment of mice bearing Ang-2-transfected tumors with the neutralizing anti-VEGF antibody, 2C3, reduced but did not prevent tumor growth, whereas 2C3 treatment abolished the growth of mock-transfected tumor cells. No increase in apoptosis was observed in the Ang-2 transfected tumors in mice, whereas mock transfected tumor showed increased apoptosis. These data suggested that Ang-2 might play a supplementary role to VEGF in promoting tumor angiogenesis.

 

 

Anti-VEGF antibody, 2C3, down-regulates expression of mouse VEGFR2 receptor Flk-1, inhibits tumor microvasculature and suppresses growth of orthotopic 231 breast carcinoma xenografts

 

Sophia Ran, Wei Zhang, Maria Sambade, Philip Thorpe, Southwestern Medical Center, Dallas, TX; Maryland General Hospital, Baltomore, MD.

Vascular endothelial growth factor (VEGF) is a multifunctional angiogenic growth factor that is a primary stimulant of tumor angiogenesis. We previously raised a neutralizing anti-VEGF monoclonal antibody 2C3, that blocks the interaction of human VEGF with either human or mouse VEGF-R2 (KDR/Flk-1) but not with VEGF-R1 (FLT-1). 2C3 had potent anti-tumor activity, inhibiting the growth of both newly injected and established human tumor xenografts growing subcutaneously in mice. In the current study, we tested the therapeutic effects of 2C3 on tumor growth in an orthotopic model of MDA-MB-231 human breast carcinoma implanted in the mammary fat pads (MFP) of nude mice. Administration of 2C3 to mice with 100-150 mm3 tumors inhibited tumor growth up to 75%, as compared to recipients of the isotype-matched irrelevant control IgG, C44. 2C3 treatment also inhibited the establishment of tumor colonies and reduced tumor burden in the lungs of mice injected intravenously with 231 cells. No toxicity of the antibody to the mice was observed. The effect of 2C3 on tumor angiogenesis was evaluated immunohistochemically. The mean microvascular density (MVD) of tumors in 2C3-treated mice was 55.71± 4.7 per mm2, as compared to 187.7 ±5.1 per mm2 in the C44-treated control group. The decrease in MVD closely correlated with degree of inhibition of tumor growth (p<0.001), suggesting that in this model human VEGF plays a predominant role in driving murine angiogenesis. The treated tumors mostly contained mid-size and large vessels. Microvessels were mainly confined to the peripheral layer bordering with normal MFP epithelium. Treatment did not affect MVD of fat and skin surrounding the tumor, indicating a specific elimination of tumor vasculature. The remaining tumor vessels showed a significantly decreased expression of VEGF-R2, as was determined by double labeling using rat anti-Flk-1 and biotinylated anti-CD31 antibodies. This observation indicates that neutralization of VEGF by 2C3 causes down-regulation of VEGF-R2 as a secondary event. This, in turn, may limit re-initiation of angiogenesis triggered by either human or mouse VEGF and render the tumor dormant for prolonged periods of time. These findings suggest that 2C3 is a candidate for treating primary cancer and for preventing the outgrowth of tumor metastases in cancer patients. Research was supported in part by Susan. G. Komen Breast Cancer Foundation.

 

 

Increased exposure of anionic phospholipids on the surface of activated endothelial cells and tumor blood vessels

 

Sophia Ran, Amber Downes, Philip E. Thorpe, Southwestern Medical Center, UT at Dallas, Dallas, TX.

Anionic phospholipids (AP) of the plasma membrane consist of phosphatidylserine (PS), phosphatidylinositol (PI), phosphatidic acid (PA) and phosphatidylglycerol (PG). PS comprises 3-7% of the total phospholipids and is exclusively located on the inner leaflet of the plasma membrane under normal circumstances. Other AP are present in much lesser quantities in the plasma membrane. PA is located mainly on the external leaflet whereas PI is located mainly on the internal leaflet. Annexin V, which specifically reacts with AP, does not bind to the external surface of normal quiescent cells, suggesting that the overall distribution of AP is heavily biased toward the inner leaflet of the plasma membrane. Externalization of PS, and annexin V binding, occurs upon cell activation, injury, apoptosis and malignant transformation. We postulated that tumor-derived factors might damage tumor endothelium and increase exposure of PS and possibly other AP. To test this hypothesis, we generated a monoclonal antibody, 9D2, that was specifically reactive with PS, PI and PA but not with other phospholipids. 9D2 is more specific for AP than is annexin V, which, strongly binds to phosphatidylethanolamine (PE) in addition to other AP. 9D2 and annexin V did not bind to cultured endothelial cells under normal circumstances. However, treatment of the cells with thrombin, inflammatory cytokines, hydrogen peroxide, hypoxic or acidic conditions induced binding of 9D2 and annexin V. Treatment with hydrogen peroxide resulted in the highest AP exposure. No binding was observed when intact endothelial monolayers were treated with a variety of other factors (VEGF, bFGF, etc) or medium alone. Combined treatment with inflammatory cytokines and hypoxia had greater than additive effects, suggesting that factors may interact to give amplified effects on AP exposure on tumor endothelium in vivo. To determine biodistribution of 9D2 and annexin V in tumor bearing mice, their localization was determined immunohistochemically after intravenous injection. 9D2 and annexin V were found on tumor blood vessels, in necrotic tumor regions and on individual malignant cells. Both reagents did not localize to normal endothelium. Isotype-matched control antibodies did not bind detectably to tumor or normal tissues. These results indicate that AP are present on the external surface of tumor endothelium but not on normal endothelium, and that AP exposure might be mediated by thrombin, hypoxia, cytokines and hydrogen peroxide. The externalized AP on the tumor endothelium could potentially be utilized for tumor vessel targeting and imaging.

 

4 April 2002

 

Differences between Thorpe and Epstein's work on the tissue-factor induced tumor clotting. The simplest explanation is as follows: Tumor capillary beds (the endothelial cells) are notorious for expressing certain types of lipids that contain negative charges. This expression promotes a "clotting" situation, since proteins of the clotting cascade (a series of binding and enzymatic properties of serum proteins that result in a blood clot) need this negatively-charged surface to start the clotting sequence. Tissue factor (and truncated Tissue Factor, tTF) easily bind to these surfaces and start the clotting process.

Thorpe originally exploited this process by delivery of TF or tTF to the tumor-associated endothelum by coupling TF to antibodies that would find targets in the endothelium, notably, V-CAM-1, an adhesion molecule found on endothelium, or prostate-specific membrane antigen (PSMA), or even the VEGF-receptor complex found on endothelium. This was his original basis for VTA. It is speculated now…with the talk of the anti-phosphatidylserine antibodies (the PS antibody) that this is another form of delivery, since PS itself is one of those negatively-charged lipids (but difficult to raise antibodies against). So there are several ways to deliver TF or tTF.

Epstein has now taken another step, in creating fusion peptides between tTF and several delivery vehicles known to get into the tumor microenvironment (via the blood vessels). He describes the use of TNT (targeting necrotic regions of the tumor), chTV-1, an antibody that targets a membrane antigen of tumor blood vessels, and a protein called RGD, which is nothing more than a small protein that binds to exposed adhesion molecules on endothelium. So, in essence, the delivery of the TF (or perhaps other targeting molecules, such as toxins) to the blood vessels is only as good as the specific targeting of the delivery molecule…in this case, a variety of antibodies or fusion-peptides
.

 

12 April 2002

 

Overview: Although the AACR every year shows much progress in exotic techniques of gene regulation involved with cancer (such as more sophistication using DNA-chip arrays and proteomics), the meeting was somewhat "stagnant" with respect to novel ideas of therapy. For example, we seem to be able to identify hundreds subtle (and not so subtle) changes in gene expression and regulation in tumor cells but we don't seem so sure which gene products are viable targets for therapy. However, molecular targeting in the realm of new toxic therapies for cancer cells (in the spirit of Gleevec, the powerful inhibitor of a needed enzyme in some leukemia and gastric cancer cells) has emerged as the concept, which is dogma for investigators trying to find specific approaches to stopping the growth of cancer.

There is little doubt that the concept and field of antiangiogenesis is rapidly being incorporated into mainstream therapeutics. However, the data from the number of papers this year dealing with "inhibition of tumor growth" using various compounds that supposedly inhibit the vascularization of tumors clearly indicate that, at the present time, inhibitors of angiogenesis are not impressive as single-agent therapy. This year, a great number of papers indicated that the best therapy with antiangiogenics is combination therapy. This further supports the growing realization that a two-compartment approach to cancer therapy, i.e., cytotoxic compounds delivered to the bulk of disease together with AI's is where the field is headed. This holds true for direct inhibitors of endothelial cell function, such as angiostatin or endostatin, as well as the indirect inhibitors such as antibodies against growth factors and their receptors that may be found on tumor-associated blood vessels. There are now a growing number of studies that demonstrate solid preclinical evidence that inhibitors of needed growth factors and survival factors of blood vessels (and tumor cells) combined with conventional cytotoxic therapies can be very powerful in the rodent models; and these combinations are making their way to the clinic.

Regarding the direct targeting of endothelial cells with VTA approaches (which is different in some respects than "inhibiting the formation of new blood vessels", in my opinion, it is too early in the preclinical studies to make great judgments as to how these studies will evolve. As with all new approaches, there are "windows" of opportunity and interest in these approaches and if they don't rapidly move from the animal quarters to the clinic, they get lost in the shuffle. It's just the way it is.

 

Epstein is a very personable scientist who grinds out most of the papers himself and has a busy lab of students and post-docs. The LEC/chTNT-3 fusion peptide study (highlighted in the AACR press release) was extremely interesting. The nature of the "humanized" portion of the fusion peptide prevents too many injections of this peptide in mice (they will build their own antibodies to it), but with 3-5 injections of this immunomodulatory molecule (stimulating a local inflammatory reaction with migration of many immune cells into the tumor area), Epstein was able to demonstrate strong inhibition of tumor growth in several animal models (renal cell, colon and lung cancer). The criticism remains that while concepts are being developed (and I suppose, the patent pool expanded), the reality remains of getting these type of molecules into clinical trials. The study using targeted tissue factor fusion peptides by Epstein (presented by Peisheng Hu, who is the scientist involved intimately with the China trials) was fascinating because one always likes to see tumors blasted in their wallow of clotted blood and dying from the inside out. Something clinically pleasant about a collapsing, dying tumor. The one construct using a simple peptide sequence (the RGD) was not impressive, but the other two, the chTV-1 and the use of the chTNT-3 as a delivery agent for the truncated tissue factor was impressive and resulted in strong intra-tumor clotting and collapse of various animal tumors. It would be very exciting to see this sort of therapy tried as single agent targeting (together with whatever Thorpe has in mind with the anti-PS antibody), but we wait the resources, I suppose, to see some fruition in that area.

I spent a lot of time looking at immunological approaches to cancer, where the excitement remains in complex studies of dendritic cells (cells that present tumor antigens to lymphocytes) and immunotherapy of cancer remains elusive and artsy-craftsy.

There was no real "breakthrough buzz" at this AACR, which is not that unusual. But the clinical potential of PPHM remains just that, potential. These areas of Thorpe and Epstein remain the science of PPHM (also found in the other papers of these two scientists at AACR), but without absolute solid clinical results from Cotara in glioblastoma, encouragement from the other Phase I studies using Cotara, or validation of the approach via China and lung cancer…all of this science remains potential. I don't put a lot of confidence in patents or potential, just clinical results.

 

On this latter point, the abstracts of Thorpe were interesting…and P. Thorpe manned his posters with great interest from the attendees and he pressed the flesh with good comments to questions that were asked. I was disappointed in the presentation from Thorpe's associate (S. Ran) on the exposure of phosphatidylserine (PS) on the surface of tumor blood vessels, in that their presentation did not contain any therapy data…(but Thorpe did comment on the other side of the room where is was…that the antibodies are effective against tumors in the mouse models). It appeared that just preferred not to show that data, which surprised me. The use of the 2C3 antibody did strongly inhibit the growth of breast carcinoma cells in mice (and lung metastasis of these cells) but I suspect this form of therapy (as with all the antibodies to growth factor receptors) would be greatly enhanced when combined with a chemotherapy. I would like to see that sort of data. It would probably represent the fastest, most effective clinical proof of a pipeline product.

Thorpe's collaborative effort with M. Rosenblum on the use of the VEGF/gelonin toxin (this is where the toxic molecule, gelonin, is brought to the tumor and blood vessels by attachment to VEGF, the growth factor and this complex binds the receptor) was interesting but the concept or data was not entirely new from a clinical point of view. If it is a viable, good therapy, then clinical trials should be in order. Some say later this year (via SUPG?).

 

05/22/2002

 

Big pharmas have drug-discovery departments that work closely with people who do the animal models of tumors. Hence, new drugs are evaluated quickly as to their toxicity and efficacy in standard preclinical models. These people are very aware of innovative methods of drug delivery and new trends of drug development. In that sense, there is little doubt that some will be quite aware of Epstein's work in the area of using TNT-fusion peptides that alter permeability of blood vessels that allow enhanced local concentration of toxic drugs within tumors. Epstein has several papers on this and related topics.

It would be helpful if PPPH had this ASCO poster on it's website, but I do not see it at the present time. Raw data of uptake and inhibition of tumor growth would make it easier to form opinions about the study presented at ASCO.

Several thoughts come to mind about what is known from the generalized statements found in the Epstein abstract. Regarding the 3 types of responses; there is little doubt that improved local delivery of the drugs to drug-sensitive tumors is a preferred method of chemotherapy. This could be utilized by enhanced local concentration of drug given at the normal (near MTD) dosing, or even using reduced doses with the same effects (I doubt this would be done clinically, rather treatment options would prefer the MTD dose to achieve greater tumor cell kill). The last two groups seem to differ in the following manner. First, "those tumors which normally do not respond to a given drug (ex. MAD 109 lung carcinoma treated with Taxol) were now found to have a significant response…" suggests that the basis of their drug-resistance did not lie in inherent properties of the tumor cells themselves, but in the lack of drug delivery to the tumor. This is a surprising result. Evidently, administration of the TNT-fusion peptide altered the local permeability or homed to distinct regions of the tumor otherwise not accessible to Taxol in the local circulation This result is distinct to the "type 3" response, described by "those tumors resistant to a given drug…remained unaffected or had only a minor response by pretreatment [with the TNT-fusion peptide]". Drug-resistant tumor populations evolve by prior drug therapy or can be inherently resistant due to the upregulation of molecular pathways that defeat the mode of action of the toxic drug. Therefore, this finding is not unexpected for pure drug-resistant tumor cells.

Eventually, these findings will be evaluated by big pharma, just as the VTA (via Thorpe) needs to be evaluated by companies able to begin meaningful, large-scale Phase I trials to prove the innovative features (with subsequent efficacy). As with many of the PPHM techniques, they have been around for many years and yet have not been translated to the clinic.

 

6/03/2002

 

Research and development of new therapeutic agents for cancer take millions of dollars. And time. I personally know of several innovative compounds that were not pursued in a clinical trial due to the extremely high cost of bringing such a compound to market in light of a limited patient population that might have received limited benefit. The realities of this type of drug development (are) fearsome. These companies are not developing cough medicine or healing cold sores one day faster by subjective analysis, but attempting to alter the natural course of malignant disease by methods that demand objective evaluation and endpoints of regression, inhibition of tumor growth, time to progression of disease, survival, and quality of life, with acceptable toxicity. Several principles must be established in studying innovative methods of cancer therapy. First, it is important to remember that, (a) THERAPY SELECTS FOR RESISTANCE; i.e., the act of targeting tumor cells by chemotherapy will result in a subpopulation of cells that are resistant to the drug, or resistant to the concentration of drug that can be safely administered to a patient, this concept holds true for beam-directed and local irradiation, (b) THE MORE UNIQUE THE TARGET IS TO CANCER CELLS, THE BETTER THE THERAPY, i.e., the more dependence that a cancer cell has on a metabolic pathway (enzymes, growth factor receptors, antiapoptotic factors, etc) to survive compared to normal cells, the better targeting can be accomplished for a compound that targets that unique pathway (best example Gleevic, STI-571), (c) IT IS NECESSARY TO IDENTIFY NON-MUTABLE TARGETS; tumors are extremely heterogenous with respect to the emergence of subpopulations of cells that are endowed with new and unique characteristics that allow them to modify and change the environment around them (including their endothelium, the blood vessel cells that supply them nutrients) and the more that a given therapy depends upon a property of tumor cells that can be easily mutated (to escape the killing), then a given therapy will be less effective.

 

Toward this type of therapeutic philosophy, PPHM has captured the methodology and patents of two very talented scientists, Drs. Epstein and Thorpe; whose approaches are quite different but based upon similar premises. Namely, that they have been able to identify vulnerabilities of tumor cells (or their blood supply) that may be very unique, at least, to the expansion of the tumor mass (the property of having necrotic regions and the need for an expanding blood supply). Dr. Epstein has targeted a basic protein subset that is found exposed in necrotic regions of tumors (the target of the TNT family of antibodies and the Lym-1 antigen found almost exclusively on B-cell lymphomas) and Dr. Thorpe has found unique antigens that are found almost exclusively on tumor-associated blood vessels (the TNT technology has reached the clinic in various formats; the Vascular Targeting of Thorpe has not).

The progress of these agents within the clinic was undertaken by PPHM over the past two decades through times of promise and despair, mainly in terms of the funding needed to complete such expensive clinical trials. Simultaneously with this type of innovative science, new formulations of targeted therapy have arisen in the possession of cash-rich pharmaceutical companies able to pursue large, multi-center trials with agents that appear to attempt to achieve that exclusive targeting of cancer cells or their blood vessels. The competition is extremely tough and requires that clinicians recognize the value of the therapy being tested and the funds to push the trials to fruition.

Toward this goal, there are recognized steps of progress that can be objectively measured. Steps of progress that give encouragement and hope to patients (and investors). First, the publication of new and encouraging preclinical data that demonstrate the proof of principle and promise of a given therapy. Toward that end, Epstein and Thorpe have published for many years the various themes of targeting DNA-histones (TNT) and vascular antigens (delivery of truncated tissue factor, antiVEGF-complex antibodies, and now the elusive anti-phosphatidylserine moiety found on tumor-associated blood vessels). Secondly, there must be well-designed and executed clinical trials of Phase I and II that promote the therapy to a serious evaluation of showing improved survival and freedom from disease and enhancement of quality of life that patients hope and pray for…and this appears to be on-track for TNT in glioblastoma and nowhere to be found for VTA.

 

The clinical trials of Oncolym, a promising radiolabeled antibody that could have easily rivaled Rituxan and Zevalin (and Bexxar) for therapy of B-cell lymphoma seems lost. In my opinion, this modality will not be recovered.

Now, in examining the state of the science for TNT and VTA and VEA, I perceive the following:

 

(a)       TNT in glioblastoma obviously lacks funding for the start of Phase III. That's my opinion. Why? The FDA has approved the Phase II progress, helped in the requirements for evaluation in Phase III, granted Orphan Status and denoted Fast-Track Phase III. A multi-center study here and in Europe will cost millions of dollars. The start has been delayed, (I assume).

 

(b)       There is no visibility of TNT in glioblastoma in the mainstream brain cancer centers. Why? Because there has been no publication of exciting, promising Phase II data by Patel or his colleagues from the collaborative centers. There has been no academic publication of Phase I or Phase II studies that were described at ASCO over a year ago;

 

(TUSTIN, Calif. - May 14, 2001--Peregrine Pharmaceuticals Inc. (Nasdaq:PPHM - news) today announced Dr. Sunil Patel, associate professor of neurosurgery at the Medical University of South Carolina, presented preliminary efficacy and safety results from a Phase II brain cancer trial using Cotara(TM), Peregrine's Tumor Necrosis Therapy drug. Patel presented his findings at the American Society of Clinical Oncology's (ASCO) 37th annual meeting, being held in San Francisco, where he was representing the Cotara brain tumor study consortium. The primary objective of the Phase II Cotara study is to determine the median time to progression of treated patients compared with a historical control population. Patel presented data on the first 29 patients in the study. This group possessed a uniformly poor prognosis, the majority of them having been diagnosed with recurrent glioblastoma multiforme (GBM), which is a form of malignant brain tumor. Primary side effects of the Cotara infusion were well tolerated in this patient population. The overall median time to progression was 13.9 weeks, despite inclusion of many heavily pretreated patients).

 

(c)        There has been no abstract or conference presentation of the sophisticated methods of image-guided catheterization of glioma treatment as described almost a year ago (Peregrine Pharmaceuticals and Image-Guided Neurologics Agree to Study Use of Navigus® Array Catheter in Treatment of Brain Cancer New Catheter May Enhance Delivery of Targeted Cancer Therapy; 22-Aug-2001) and there has been no publication of the findings of Phase I trials in any of the solid tumors treated in Mexico or Stanford or the Mayo Clinic (26-Jun-2001, TUSTIN, Calif.--[BW HealthWire] Peregrine Pharmaceuticals Inc. (Nasdaq:PPHM - news) today announced preliminary results from a Phase I/II Malignant Tumor Trial utilizing Cotara, Peregrine's Tumor Necrosis Therapy (TNT) drug; PEREGRINE ANNOUNCES OPENING OF A NEW STUDY IN HEPATIC CANCER New trial to explore use of CotaraTM along with ablation of hepatic tumors , 19-Apr-2001, PEREGRINE OPENS STANFORD UNIVERSITY TRIAL TO STUDY CANCERS OF THE PANCREAS AND BILIARY SYSTEM Trial to explore new uses of CotaraTM, 12-Apr-2001, PEREGRINE ANNOUNCES OPENING OF A NEW STUDY AT THE STANFORD UNIVERSITY, STANFORD, CA New trial to explore use of CotaraTM in soft tissue sarcoma, 9-Apr-2001).

 

When there are no publications, there are two interpretations.

 

(1)       The data are not worth writing up for the academic oncology community.

 

(2)       There is no pressure on the investigators to publish their clinical research.

 

Both of these conclusions are extremely unlikely. There must be some informative techniques and knowledge gained from these studies and these investigators must certainly feel an obligation to their academic careers to publish good clinical research. Why these data are not published is a very disturbing mystery.

Epstein presented interesting data at ASCO on the properties of VEA, using the fusion peptide of the permeability portion of the IL-2 molecule fused to the TNT antibody binding site, but he has published on this concept for several years. It must now reach the clinic or be lost in the bin of many good papers and ideas that never reach fruition. Thorpe presented interesting data at AACR on the exposure of phosphatidylserine on blood vessels, but gave NO data as to the potential use in the clinic. Very disappointing. We have heard nothing on the use of truncated tissue factor as a therapeutic weapon against tumor.

And then there are the other collaborations and partnerships (I don't know what to call them) that never seem to have a publication about anything, such as the SUPG deal, which has floated around the table for a long, long time, (Peregrine Pharmaceuticals and SuperGen Inc. Announce Finalization of Licensing Deal for VEGF Vascular Targeting Agents 13-Feb-2001),

 

and the possibility of using TNT antibodies as a targeting agents coupled to liposomes to deliver antitumor agents to the interior of tumor cells, a simple concept that has no literature (Tustin, CA - July 30, 2001- Peregrine Pharmaceuticals (NASDAQ: PPHM) today announced the signing of a Joint Development Agreement with Oakwood Labs, Oakwood Village, Ohio. Under the terms of the agreement, the companies will jointly evaluate therapeutic agents that combine Peregrine’s Tumor Necrosis Therapy (TNT) tumor targeting technology with Oakwood’s anti-cancer Liposome technology. Under the agreement, Peregrine will provide TNT antibodies and Oakwood will provide liposomes and preclinical testing resources. At the completion of preclinical testing, Peregrine and Oakwood will decide whether to advance the potential products into human clinical studies under a commercialization agreement).

 

In addition, the imaging possibilities that the TNT antibodies offer due to local delivery within the tumor environment, but of course, no publications on this concept (PEREGRINE ANNOUNCES RESEARCH AND DEVELOPMENT AGREEMENT WITH PAUL SCHERRER INSTITUTE FOR TNT BASED PET IMAGING AGENTS Continues Radiolabeling Research and Development 23-Mar-2001),

 

or the exciting prospect of cytokine-fusion peptides described by Epstein for several years and awaiting discovery within a clinical setting ( TECHNICLONE AND MERCK KGAA SIGN AGREEMENT ON USE OF TUMOR NECROSIS THERAPY (TNT) TECHNOLOGY 23-Oct-2000).

Finally, the confusing aspect of biotech disclosure. Within the confines of the Society of Nuclear Medicine meeting this month was found two abstracts from China dealing with the long awaited and greatly elusive data on therapy of lung cancer and liver cancer. These data were explicitly embargoed for release until the day of presentation by the SNM meeting directors, and the abstracts could not be viewed until May 7th, 2002, at which time, PPHM made a startling announcement of the results and comments by Epstein (7 May 2002, PEREGRINE PHARMACEUTICALS ANNOUNCES ABSTRACTS OF INTERIM RESULTS FROM TUMOR NECROSIS THERAPY TREATMENT OF LUNG AND HEPATIC CANCERS Data to be presented at Society of Nuclear Medicine's 49th Annual Meeting, June 15-19, 2002). The data, in abstract form, seem to contain a small amount of patients, in light of the common knowledge that this form of therapy had been taken place for years in China, and very difficult to evaluate. So we await these findings, the implications of which are nothing more than absolute validation or refutation of the entire concept of TNT-based therapy, in my opinion. So June in an important month, yes. Since we have no other clinical barometer by which to evaluate the validity of TNT nor information as to the start of VTA, license of VEA, demise (?) of Oncolym, or hope of TNT in Phase III.

 

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